{"id":891,"date":"2025-05-07T12:48:33","date_gmt":"2025-05-07T09:48:33","guid":{"rendered":"https:\/\/wiki.voka.io\/diseases\/uncategorized\/paraganglioma\/"},"modified":"2025-12-09T12:57:02","modified_gmt":"2025-12-09T09:57:02","slug":"paraganglioma","status":"publish","type":"diseases_post","link":"https:\/\/wiki.voka.io\/pt\/doencas\/vasculares\/paraganglioma\/","title":{"rendered":"Chemodectoma (paraganglioma): etiologia, patog\u00e9nese, classifica\u00e7\u00e3o, diagn\u00f3stico, m\u00e9todos de tratamento"},"content":{"rendered":"<p>O <span class=\"glossary-term\" data-title=\"Tumor gl\u00f4mico\" data-tooltip=\"O tumor gl\u00f4mico, ou paraganglioma, \u00e9 um tumor raro, geralmente benigno, que se desenvolve a partir das c\u00e9lulas dos parag\u00e2nglios (quimiorreceptores). Essas c\u00e9lulas respondem normalmente \u00e0s altera\u00e7\u00f5es da composi\u00e7\u00e3o qu\u00edmica do sangue e est\u00e3o localizadas ao longo dos principais vasos e nervos.\" data-link=\"https:\/\/wiki.voka.io\/pt\/glossario\/tumor-glomico\/\">paraganglioma<\/span> da car\u00f3tida (quimiodectoma) \u00e9 um tumor raro, maioritariamente benigno, que surge das c\u00e9lulas quimiorreceptoras do corpo carot\u00eddeo localizado na bifurca\u00e7\u00e3o da art\u00e9ria car\u00f3tida comum.<\/p>\n<figure class=\"wp-block-image size-large\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/Vascular%20Pathology\/%20Chemodectoma\/Hemodectoma_main%20(1).webp\" alt=\"Chemodectoma (paraganglioma)\"><figcaption class=\"wp-element-caption\">Chemodectoma (paraganglioma)<\/figcaption><\/figure>\n<h2 class=\"wp-block-heading\" id=\"epidemiologia\">Epidemiologia <\/h2>\n<ul class=\"wp-block-list\">\n<li>Aproximadamente 1-2 casos por 100.000 habitantes.<\/li>\n<li>As mulheres s\u00e3o mais frequentemente afectadas do que os homens.<\/li>\n<li>A idade m\u00e9dia do diagn\u00f3stico \u00e9 de cerca de 45 anos.<\/li>\n<li>A preval\u00eancia \u00e9 elevada nos pa\u00edses da Am\u00e9rica Latina, especialmente no M\u00e9xico, onde as mulheres representam at\u00e9 90% dos casos.<\/li>\n<li>Os habitantes de zonas de altitude elevada t\u00eam um risco acrescido de desenvolver quimiodectomas devido \u00e0 hip\u00f3xia cr\u00f3nica.<\/li>\n<\/ul>\n<h2 class=\"wp-block-heading\" id=\"a-etiologia\">A etiologia<\/h2>\n<p>Muta\u00e7\u00f5es <strong>gen\u00e9ticas<\/strong>: As muta\u00e7\u00f5es nos genes que codificam as subunidades do complexo succinato desidrogenase (SDH), que est\u00e1 envolvido na cadeia respirat\u00f3ria mitocondrial e no metabolismo celular, desempenham um papel importante. Os principais genes s\u00e3o:  <\/p>\n<ul class=\"wp-block-list\">\n<li><strong>SDHD<\/strong> \u2013 mais frequentemente associada a paragangliomas m\u00faltiplos da cabe\u00e7a e do pesco\u00e7o; transmitida por via paterna;<\/li>\n<li><strong>SDHB<\/strong> \u2013 associado a formas mais agressivas e a um maior risco de evolu\u00e7\u00e3o maligna;<\/li>\n<li><strong>SDHC, SDHA e SDHAF2<\/strong> est\u00e3o menos frequentemente envolvidos, mas podem tamb\u00e9m contribuir para o desenvolvimento de tumores.<\/li>\n<\/ul>\n<p><strong>S\u00edndromes<\/strong> associadas a quimiodectomas: <\/p>\n<ul class=\"wp-block-list\">\n<li>S\u00edndrome de Von Hippel-Lindau (VHL); <\/li>\n<li>Neoplasia end\u00f3crina m\u00faltipla tipo 2 (MEN2); <\/li>\n<li>Neurofibromatose tipo 1 (NF1).<\/li>\n<\/ul>\n<p><strong>Hip\u00f3xia cr\u00f3nica<\/strong>: viver a > 2000 m acima do n\u00edvel do mar, bem como condi\u00e7\u00f5es como a doen\u00e7a pulmonar obstrutiva cr\u00f3nica e a doen\u00e7a card\u00edaca cong\u00e9nita, podem estimular a hiperplasia do corpo carot\u00eddeo.<\/p>\n<p>Hist\u00f3ria familiar: cerca de 10% dos casos s\u00e3o familiares.<\/p>\n<figure class=\"wp-block-video\" id=\"animacao-3d-quimiodectoma-tipo-i\"><video controls><source data-src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/Vascular%20Pathology\/%20Chemodectoma\/chemodectoma-type-1.webm\" type=\"video\/webm\"><\/source><\/video><figcaption class=\"wp-element-caption\">Anima\u00e7\u00e3o 3D \u2013 Quimiodectoma tipo I<\/figcaption><\/figure>\n<figure class=\"wp-block-video\" id=\"animacao-3d-quimiodectoma-tipo-iii\"><video controls><source data-src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/Vascular%20Pathology\/%20Chemodectoma\/chemodectoma-type-3.webm\" type=\"video\/webm\"><\/source><\/video><figcaption class=\"wp-element-caption\">Anima\u00e7\u00e3o 3D \u2013 Quimiodectoma tipo III<\/figcaption><\/figure>\n<h2 class=\"wp-block-heading\" id=\"patogenese\">Patog\u00e9nese<\/h2>\n<ol class=\"wp-block-list\">\n<li><strong>Muta\u00e7\u00f5es heredit\u00e1rias (SDHx)<\/strong><\/li>\n<\/ol>\n<p><strong>Muta\u00e7\u00f5es da SDH<\/strong> (enzima-chave do complexo II da cadeia respirat\u00f3ria mitocondrial e do ciclo de Krebs) \u2192 Acumula\u00e7\u00e3o <strong>de succinato<\/strong> (actua como \u201concometabolito\u201d) \u2192 <strong>Inativa\u00e7\u00e3o das enzimas prolil hidroxilases<\/strong> (PHDs), controlando a degrada\u00e7\u00e3o do HIF-1\u03b1 (fator induzido pela hip\u00f3xia) \u2192 <strong>Acumula\u00e7\u00e3o de HIF-1\u03b1<\/strong> \u2192 <strong>Pseudo-hip\u00f3xia <\/strong>\u2192 <strong>Ativa\u00e7\u00e3o de VEGF<\/strong> (angiog\u00e9nese)\/ <strong>GLUT1 <\/strong>(glic\u00f3lise)\/ <strong>PDGF <\/strong>(prolifera\u00e7\u00e3o celular) \u2192 <strong>Transforma\u00e7\u00e3o neopl\u00e1sica das<\/strong> c\u00e9lulas quimiorreceptoras e forma\u00e7\u00e3o de tumores.<\/p>\n<ol start=\"2\" class=\"wp-block-list\">\n<li><strong>Hip\u00f3xia cr\u00f3nica<\/strong><\/li>\n<\/ol>\n<p>Hip\u00f3xia (altitude, DPOC) \u2192 Diminui\u00e7\u00e3o da pO\u2082 \u2192 Ativa\u00e7\u00e3o do recetor carot\u00eddeo \u2192 Hiperplasia celular \u2192 Acumula\u00e7\u00e3o de HIF-1\u03b1 \u2192 Angiog\u00e9nese e neoplasia.<\/p>\n<p>Como resultado, o tumor aumenta gradualmente de tamanho. \u00c0 medida que cresce, pode demonstrar um car\u00e1cter localmente invasivo, a ponto de circundar ou comprimir estruturas anat\u00f3micas pr\u00f3ximas, como as art\u00e9rias car\u00f3tidas interna e externa, os nervos vago, hioide e lingual, o que pode causar sintomas neurol\u00f3gicos e vasculares associados. <\/p>\n<h2 class=\"wp-block-heading\" id=\"classificacao-do-paraganglioma\">Classifica\u00e7\u00e3o do paraganglioma<\/h2>\n<p><strong>W.R. Shamblin<\/strong> prop\u00f4s dividir os paragangliomas da car\u00f3tida da panturrilha em tr\u00eas tipos:<\/p>\n<ul class=\"wp-block-list\">\n<li>Tipo I: tumores limitados at\u00e9 3,5 cm, vagamente associados \u00e0s paredes arteriais;<\/li>\n<li>Tipo II: 3,5-5 cm, cobrem parcialmente as art\u00e9rias car\u00f3tidas, t\u00eam uma fus\u00e3o mais densa com as paredes arteriais;<\/li>\n<li>Tipo III: mais de 5 cm, cobrindo as art\u00e9rias car\u00f3tidas e\/ou vasos pr\u00f3ximos, os nervos t\u00eam uma fus\u00e3o acentuadamente densa com estas estruturas.<\/li>\n<\/ul>\n<p>Al\u00e9m disso, o quimiodectoma pode ser classificado de acordo com a etiologia: espor\u00e1dico (at\u00e9 85%), familiar (10-15%) e hiperpl\u00e1sico (1-5%).<\/p>\n<figure class=\"wp-block-image size-large\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/Vascular%20Pathology\/%20Chemodectoma\/Hemodect_1_type.webp\" alt=\"Chemodectoma tipo I\"><figcaption class=\"wp-element-caption\">Hemodectoma tipo I \u2013 <a href=\"https:\/\/catalog.voka.io\/en\/models\/6e2f9dc5-6e91-46c4-b881-b038f53acd05\/6ec65686-8390-42c1-b3f3-c7a1f7148948\/aa66bddd-72b2-4945-91b8-90210e91fc55\/9db48cfc-4d8c-4de0-8e9c-e20a7d131626\" target=\"_blank\" rel=\"noreferrer noopener nofollow\">Modelo 3D<\/a><\/figcaption><\/figure>\n<figure class=\"wp-block-image size-large\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/Vascular%20Pathology\/%20Chemodectoma\/Hemodectoma_3_type.webp\" alt=\"Quimiodectoma tipo III\"><figcaption class=\"wp-element-caption\">Hemodectoma tipo III \u2013 <a href=\"https:\/\/catalog.voka.io\/en\/models\/6e2f9dc5-6e91-46c4-b881-b038f53acd05\/6ec65686-8390-42c1-b3f3-c7a1f7148948\/aa66bddd-72b2-4945-91b8-90210e91fc55\/f2482b21-b370-4e72-8b94-4443d26df1f7\" target=\"_blank\" rel=\"noreferrer noopener nofollow\">Modelo 3D<\/a><\/figcaption><\/figure>\n<h2 class=\"wp-block-heading\" id=\"manifestacoes-clinicas\">Manifesta\u00e7\u00f5es cl\u00ednicas<\/h2>\n<p>Durante muito tempo, pode n\u00e3o haver sintomas. \u00c0 medida que o tumor cresce, podem surgir queixas:  <\/p>\n<ul class=\"wp-block-list\">\n<li><strong>Tumor palp\u00e1vel<\/strong>: massa de crescimento lento, indolor e puls\u00e1til na superf\u00edcie lateral do pesco\u00e7o (na zona do m\u00fasculo esternoclavicular-papilar);<\/li>\n<li><strong>Sintomas neurol\u00f3gicos<\/strong>: rouquid\u00e3o da voz, disfagia, dorm\u00eancia da l\u00edngua causada pela compress\u00e3o dos nervos cranianos (IX-XII);<\/li>\n<li><strong>Queixas relacionadas com a produ\u00e7\u00e3o de catecolaminas<\/strong> (palpita\u00e7\u00f5es, ataques de hipertens\u00e3o arterial, suores, dores de cabe\u00e7a, tremores);<\/li>\n<li>Raramente:<strong> tonturas, s\u00edncope<\/strong> com compress\u00e3o do seio carot\u00eddeo.<\/li>\n<\/ul>\n<h2 class=\"wp-block-heading\" id=\"diagnostico-do-paraganglioma\">Diagn\u00f3stico do paraganglioma<\/h2>\n<ul class=\"wp-block-list\">\n<li><strong>Exame f\u00edsico: <\/strong>tumor denso e palpitante no pesco\u00e7o, que se desloca horizontalmente, mas n\u00e3o verticalmente;<\/li>\n<li><strong>Ecografia com Doppler<\/strong>: tumor hipervascular na zona da bifurca\u00e7\u00e3o carot\u00eddea;<\/li>\n<li><strong><span class=\"glossary-term\" data-title=\"RM (Resson\u00e2ncia magn\u00e9tica)\" data-tooltip=\"A resson\u00e2ncia magn\u00e9tica (RM) \u00e9 uma t\u00e9cnica de imagem moderna n\u00e3o invasiva que produz imagens em camadas altamente detalhadas de \u00f3rg\u00e3os e tecidos internos. O m\u00e9todo baseia-se no fen\u00f3meno da resson\u00e2ncia magn\u00e9tica nuclear. A principal vantagem da RM \u00e9 a aus\u00eancia de radia\u00e7\u00e3o ionizante.\" data-link=\"https:\/\/wiki.voka.io\/pt\/glossario\/rm\/\">RM<\/span> com contraste<\/strong>: aspeto carater\u00edstico de \u201csal e pimenta\u201d nas imagens ponderadas em T1;<\/li>\n<li><strong><span class=\"glossary-term\" data-title=\"Tomografia computorizada\" data-tooltip=\"A tomografia computadorizada \u00e9 um exame de imagem que usa raios X para obter imagens transversais (cortes) de \u00f3rg\u00e3os e tecidos internos. \u00c9 uma das principais t\u00e9cnicas de imagem da medicina moderna, com elevado n\u00edvel de gera\u00e7\u00e3o de informa\u00e7\u00e3o.\" data-link=\"https:\/\/wiki.voka.io\/pt\/glossario\/tc-tomografia-computadorizada\/\">TC<\/span> com contraste<\/strong>: determina\u00e7\u00e3o do grau de invas\u00e3o vascular, avalia\u00e7\u00e3o da classifica\u00e7\u00e3o de Shamblin. Constru\u00e7\u00e3o de um modelo 3D para o planeamento da cirurgia; <\/li>\n<li><strong>Angiografia<\/strong>: dete\u00e7\u00e3o do \u201csinal da lira\u201d \u2013 diverg\u00eancia das art\u00e9rias car\u00f3tidas interna e externa. Permite avaliar a necessidade\/possibilidade de <span class=\"glossary-term\" data-title=\"Emboliza\u00e7\u00e3o\" data-tooltip=\"A emboliza\u00e7\u00e3o \u00e9 um procedimento endovascular minimamente invasivo em que o m\u00e9dico bloqueie (oclui) um vaso sangu\u00edneo por meio de inje\u00e7\u00e3o de materiais especiais \u2014 agentes emb\u00f3licos \u2014 em seu l\u00famen.\" data-link=\"https:\/\/wiki.voka.io\/pt\/glossario\/embolizacao\/\">emboliza\u00e7\u00e3o<\/span> desta zona, como etapa pr\u00e9via \u00e0 interven\u00e7\u00e3o cir\u00fargica;  <\/li>\n<li><strong>PET-CT com 68Ga-DOTATATE<\/strong>: se houver suspeita de focos m\u00faltiplos ou metast\u00e1ticos; <\/li>\n<li><strong>Exames laboratoriais<\/strong>: n\u00edveis plasm\u00e1ticos e urin\u00e1rios de metanefrinas e normetanefrinas em caso de suspeita de tumor secretado;<\/li>\n<li><strong>Teste gen\u00e9tico para detetar muta\u00e7\u00f5es nos genes<\/strong> SDH na presen\u00e7a de hist\u00f3ria familiar ou de tumores m\u00faltiplos.<\/li>\n<\/ul>\n<h2 class=\"wp-block-heading\" id=\"tratamento\">Tratamento<\/h2>\n<p>O tratamento do quimiodectoma carot\u00eddeo depende do tamanho do tumor, dos sintomas cl\u00ednicos, do risco de complica\u00e7\u00f5es, da atividade funcional, do perfil gen\u00e9tico e do grau de Shamblin. As principais modalidades de tratamento s\u00e3o a excis\u00e3o cir\u00fargica, a emboliza\u00e7\u00e3o pr\u00e9-operat\u00f3ria e, em casos selecionados, a radioterapia ou a quimioterapia. <\/p>\n<ol class=\"wp-block-list\">\n<li><strong>Emboliza\u00e7\u00e3o pr\u00e9-operat\u00f3ria<\/strong><\/li>\n<\/ol>\n<p><strong>Emboliza\u00e7\u00e3o pr\u00e9-operat\u00f3ria <\/strong>para reduzir a vasculariza\u00e7\u00e3o do tumor e a perda de sangue intra-operat\u00f3ria, e para facilitar o isolamento do tumor durante a cirurgia.<\/p>\n<p><strong>Indica\u00e7\u00f5es<\/strong>:<\/p>\n<ul class=\"wp-block-list\">\n<li>Tumores de Shamblin de grau II-III;<\/li>\n<li>Di\u00e2metro do tumor >3 cm;<\/li>\n<li>Presen\u00e7a de fluxo sangu\u00edneo arterial significativo (de acordo com a TC\/angiografia);<\/li>\n<li>Ressec\u00e7\u00e3o planeada com reconstru\u00e7\u00e3o vascular.<\/li>\n<\/ul>\n<p><strong>Contra-indica\u00e7\u00f5es<\/strong>:<\/p>\n<ul class=\"wp-block-list\">\n<li>Tumores de Shamblin I;<\/li>\n<li>N\u00e3o tem componente arterial (pouca vasculariza\u00e7\u00e3o);<\/li>\n<li>Anastomoses com a circula\u00e7\u00e3o cerebral \u2013 risco de emboliza\u00e7\u00e3o cerebral.<\/li>\n<\/ul>\n<p><strong>Procedimento<\/strong>: Realiza-se uma angiografia selectiva da art\u00e9ria car\u00f3tida externa. Os agentes embolizantes s\u00e3o injectados atrav\u00e9s de um microcateter: part\u00edculas de polivinil\u00e1lcool (PVA), microesferas, menos frequentemente cola ou espirais. A angiografia de controlo confirma a redu\u00e7\u00e3o do fluxo sangu\u00edneo. A cirurgia \u00e9 efectuada no prazo de 24-48 horas ap\u00f3s a emboliza\u00e7\u00e3o, enquanto o efeito persistir.   <\/p>\n<div class=\"social-banner-block\">\n<div class=\"social-banner-content\">\n<p class=\"h5-title text-black\">Encontra mais conte\u00fados cientificamente exactos nas nossas redes sociais<\/p>\n<p><span class=\"social-banner-text text-grey\">Subscreve e n\u00e3o percas os recursos mais recentes<\/span><\/p>\n<div class=\"social-links-wrapper\"><a class=\"social-icon-link\" href=\"https:\/\/www.facebook.com\/VOKA3DAnatomyAndPathology\/\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/facebook.svg\" alt=\"social link\"><\/a><a class=\"social-icon-link\" href=\"https:\/\/www.instagram.com\/voka.io\/\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/insta.svg\" alt=\"social link\"><\/a><a class=\"social-icon-link\" href=\"https:\/\/www.linkedin.com\/company\/voka-io\/posts\/?feedView=all\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/linkedin.svg\" alt=\"social link\"><\/a><a class=\"social-icon-link\" href=\"https:\/\/www.youtube.com\/@vokaio\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/youtube.svg\" alt=\"social link\"><\/a><a class=\"social-icon-link\" href=\"https:\/\/www.pinterest.com\/voka3danatomyandpathology\/\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/pinterest.svg\" alt=\"social link\"><\/a><a class=\"social-icon-link\" href=\"https:\/\/www.tiktok.com\/@voka.io\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/tiktok.svg\" alt=\"social link\"><\/a><a class=\"social-icon-link\" href=\"https:\/\/discord.gg\/7ejUpq8DRR\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/discord.svg\" alt=\"social link\"><\/a><\/div>\n<\/div>\n<p><img decoding=\"async\" class=\"social-banner-image\" loading=\"lazy\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/social-media-banner-mobile-image.webp\" alt=\"Banner background\"><\/div>\n<ol start=\"2\" class=\"wp-block-list\">\n<li><strong>Tratamento cir\u00fargico <\/strong><\/li>\n<\/ol>\n<p><strong>Indica\u00e7\u00f5es<\/strong>:<\/p>\n<ul class=\"wp-block-list\">\n<li>Tumores sintom\u00e1ticos (dor, disfagia, perturba\u00e7\u00e3o da fala);<\/li>\n<li>Crescimento r\u00e1pido do tumor;<\/li>\n<li>Tumores >2,5-3 cm (mesmo assintom\u00e1ticos);<\/li>\n<li>Atividade confirmada por PET ou bioqu\u00edmica;<\/li>\n<li>Muta\u00e7\u00e3o SDHB confirmada (risco de malignidade);<\/li>\n<li>Idade <60 anos.<\/li>\n<\/ul>\n<p><strong>Tipos de tratamento cir\u00fargico<\/strong>:<\/p>\n<ul class=\"wp-block-list\">\n<li><strong>Ressec\u00e7\u00e3o extracapsular do tumor<\/strong>. Padr\u00e3o para Shamblin I-II, preserva\u00e7\u00e3o vascular, risco m\u00ednimo;<\/li>\n<li><strong>Ressec\u00e7\u00e3o da art\u00e9ria car\u00f3tida com reconstru\u00e7\u00e3o<\/strong>. Mais frequentemente com Shamblin III. Ap\u00f3s a ressec\u00e7\u00e3o da art\u00e9ria car\u00f3tida, \u00e9 realizada uma pr\u00f3tese (Dacron, PTFE); <\/li>\n<li><strong>Neuromonitoriza\u00e7\u00e3o e microcirurgia<\/strong>. Utiliza-se quando est\u00e1 pr\u00f3ximo dos nervos cranianos (IX-XII).<\/li>\n<\/ul>\n<p><strong>Poss\u00edveis complica\u00e7\u00f5es<\/strong>:<\/p>\n<ul class=\"wp-block-list\">\n<li>Hemorragia (especialmente em caso de emboliza\u00e7\u00e3o inadequada);<\/li>\n<li>Danos nos nervos cranianos (IX-XII) \u2013 at\u00e9 30% em tumores grandes;<\/li>\n<li>Acidente vascular cerebral (quando o fluxo sangu\u00edneo colateral \u00e9 prejudicado);<\/li>\n<li>Recidiva (rara, com ressec\u00e7\u00e3o incompleta).<\/li>\n<\/ul>\n<ol start=\"3\" class=\"wp-block-list\">\n<li><strong>Quimioterapia <\/strong><\/li>\n<\/ol>\n<p>N\u00e3o se trata de um tratamento padr\u00e3o para o quimiodectoma carot\u00eddeo, uma vez que a maioria dos tumores \u00e9 de crescimento lento e de natureza benigna. No entanto, em casos raros de evolu\u00e7\u00e3o maligna (progress\u00e3o r\u00e1pida, les\u00f5es metast\u00e1ticas) ou em formas metast\u00e1ticas inoper\u00e1veis, pode ser utilizada terapia sist\u00e9mica. <\/p>\n<ol start=\"4\" class=\"wp-block-list\">\n<li><strong>Terapia com radionucl\u00eddeos \u00b9\u2077\u2077Lu-DOTATATE (PRRT) <\/strong><\/li>\n<\/ol>\n<p>Prescrito na presen\u00e7a de express\u00e3o de receptores de somatostatina por PET com \u2076\u2078\u2078Ga-DOTATATE.<\/p>\n<div>\n<h2 class=\"faq-title h2-article\" id=\"faq\">FAQ<\/h2>\n<div class=\"faq-section\">\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">1. O quimiodectoma da car\u00f3tida \u00e9 um tumor maligno?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">Na maioria dos casos, n\u00e3o o \u00e9. Os quimiodectomas da car\u00f3tida s\u00e3o tumores benignos de crescimento lento. No entanto, na presen\u00e7a de muta\u00e7\u00f5es no gene SDHB, \u00e9 poss\u00edvel um potencial maligno com met\u00e1stases.  <\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">2. \u00c9 poss\u00edvel observar apenas um quimiodectoma da car\u00f3tida sem o remover?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">Sim, a vigil\u00e2ncia ativa \u00e9 poss\u00edvel em alguns casos, especialmente se o tumor for pequeno (<2,5 cm), assintom\u00e1tico, idoso ou se houver contra-indica\u00e7\u00f5es para a cirurgia. No entanto, se houver sinais de crescimento ou compress\u00e3o das estruturas do pesco\u00e7o, \u00e9 necess\u00e1rio tratamento. <\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">3. A cirurgia para remover um quimiodectoma da car\u00f3tida \u00e9 perigosa?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">Os riscos dependem do tamanho e da localiza\u00e7\u00e3o do tumor. No caso de grandes massas, s\u00e3o poss\u00edveis complica\u00e7\u00f5es, incluindo les\u00f5es dos nervos cranianos, hemorragias e eventos isqu\u00e9micos. A emboliza\u00e7\u00e3o pr\u00e9-operat\u00f3ria \u00e9 frequentemente efectuada para reduzir os riscos.  <\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">4. Os outros membros da fam\u00edlia t\u00eam de ser examinados se me for diagnosticado um quimiodectoma?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">Se te for diagnosticada uma muta\u00e7\u00e3o heredit\u00e1ria (por exemplo, SDHD, SDHB), recomenda-se o aconselhamento gen\u00e9tico e o rastreio dos teus familiares mais pr\u00f3ximos, uma vez que a doen\u00e7a pode ser familiar.<\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">5. Como se pode distinguir o quimiodectoma da car\u00f3tida de outros tumores do pesco\u00e7o?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">O quimiodectoma carot\u00eddeo localiza-se geralmente na bifurca\u00e7\u00e3o da art\u00e9ria car\u00f3tida comum, \u00e9 puls\u00e1til, desloca-se horizontalmente, mas n\u00e3o verticalmente, e apresenta o carater\u00edstico \u201csinal da lira\u201d na TC\/RM. O diagn\u00f3stico \u00e9 esclarecido por imagiologia e angiografia. <\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">6. Um quimiodectoma pode causar dor ou desconforto?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">Na maioria dos casos, n\u00e3o, especialmente nas fases iniciais. No entanto, \u00e0 medida que o tumor cresce, pode causar press\u00e3o nos nervos e vasos sangu\u00edneos, resultando em dor, rouquid\u00e3o, dificuldade em engolir ou tonturas. <\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">7. Existe o risco de recidiva ap\u00f3s a remo\u00e7\u00e3o do tumor?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">Se o tumor for completamente removido, o risco de recorr\u00eancia \u00e9 baixo (menos de 5%). Contudo, em caso de ressec\u00e7\u00e3o incompleta, forma heredit\u00e1ria ou presen\u00e7a de muta\u00e7\u00e3o SDHB, \u00e9 poss\u00edvel a recorr\u00eancia ou o desenvolvimento de novos focos. Nestes casos, \u00e9 importante um acompanhamento a longo prazo.  <\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<\/div>\n<p><script type=\"application\/ld+json\">\n    {\n    \"@context\": \"https:\/\/schema.org\",\n    \"@type\": \"FAQPage\",\n    \"mainEntity\": [\n        {\n            \"@type\": \"Question\",\n            \"name\": \"O quimiodectoma da car\u00f3tida \u00e9 um tumor maligno?\",\n            \"acceptedAnswer\": {\n                \"@type\": \"Answer\",\n                \"text\": \"Na maioria dos casos, n\u00e3o o \u00e9. Os quimiodectomas da car\u00f3tida s\u00e3o tumores benignos de crescimento lento. No entanto, na presen\u00e7a de muta\u00e7\u00f5es no gene SDHB, \u00e9 poss\u00edvel um potencial maligno com met\u00e1stases.  \"\n            }\n        },\n        {\n            \"@type\": \"Question\",\n            \"name\": \"\u00c9 poss\u00edvel observar apenas um quimiodectoma da car\u00f3tida sem o remover?\",\n            \"acceptedAnswer\": {\n                \"@type\": \"Answer\",\n                \"text\": \"Sim, a vigil\u00e2ncia ativa \u00e9 poss\u00edvel em alguns casos, especialmente se o tumor for pequeno (<2,5 cm), assintom\u00e1tico, idoso ou se houver contra-indica\u00e7\u00f5es para a cirurgia. No entanto, se houver sinais de crescimento ou compress\u00e3o das estruturas do pesco\u00e7o, \u00e9 necess\u00e1rio tratamento. \"\n            }\n        },\n        {\n            \"@type\": \"Question\",\n            \"name\": \"A cirurgia para remover um quimiodectoma da car\u00f3tida \u00e9 perigosa?\",\n            \"acceptedAnswer\": {\n                \"@type\": \"Answer\",\n                \"text\": \"Os riscos dependem do tamanho e da localiza\u00e7\u00e3o do tumor. No caso de grandes massas, s\u00e3o poss\u00edveis complica\u00e7\u00f5es, incluindo les\u00f5es dos nervos cranianos, hemorragias e eventos isqu\u00e9micos. A emboliza\u00e7\u00e3o pr\u00e9-operat\u00f3ria \u00e9 frequentemente efectuada para reduzir os riscos.  \"\n            }\n        },\n        {\n            \"@type\": \"Question\",\n            \"name\": \"Os outros membros da fam\u00edlia t\u00eam de ser examinados se me for diagnosticado um quimiodectoma?\",\n            \"acceptedAnswer\": {\n                \"@type\": \"Answer\",\n                \"text\": \"Se te for diagnosticada uma muta\u00e7\u00e3o heredit\u00e1ria (por exemplo, SDHD, SDHB), recomenda-se o aconselhamento gen\u00e9tico e o rastreio dos teus familiares mais pr\u00f3ximos, uma vez que a doen\u00e7a pode ser familiar.\"\n            }\n        },\n        {\n            \"@type\": \"Question\",\n            \"name\": \"Como se pode distinguir o quimiodectoma da car\u00f3tida de outros tumores do pesco\u00e7o?\",\n            \"acceptedAnswer\": {\n                \"@type\": \"Answer\",\n                \"text\": \"O quimiodectoma carot\u00eddeo localiza-se geralmente na bifurca\u00e7\u00e3o da art\u00e9ria car\u00f3tida comum, \u00e9 puls\u00e1til, desloca-se horizontalmente, mas n\u00e3o verticalmente, e apresenta o carater\u00edstico \\\"sinal da lira\\\" na TC\/RM. O diagn\u00f3stico \u00e9 esclarecido por imagiologia e angiografia. \"\n            }\n        },\n        {\n            \"@type\": \"Question\",\n            \"name\": \"Um quimiodectoma pode causar dor ou desconforto?\",\n            \"acceptedAnswer\": {\n                \"@type\": \"Answer\",\n                \"text\": \"Na maioria dos casos, n\u00e3o, especialmente nas fases iniciais. No entanto, \u00e0 medida que o tumor cresce, pode causar press\u00e3o nos nervos e vasos sangu\u00edneos, resultando em dor, rouquid\u00e3o, dificuldade em engolir ou tonturas. \"\n            }\n        },\n        {\n            \"@type\": \"Question\",\n            \"name\": \"Existe o risco de recidiva ap\u00f3s a remo\u00e7\u00e3o do tumor?\",\n            \"acceptedAnswer\": {\n                \"@type\": \"Answer\",\n                \"text\": \"Se o tumor for completamente removido, o risco de recorr\u00eancia \u00e9 baixo (menos de 5%). 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Nestes casos, \u00e9 importante um acompanhamento a longo prazo.  \"\n            }\n        }\n    ]\n}<\/script><\/div>\n<div class=\"sources-list-block sources-list-hidden\" id=\"lista-de-fontes\">\n<div class=\"sources-list-content\">\n<div class=\"sources-list-title\">\n<p class=\"small-text-bold text-black sources-list-title-text\">Lista de fontes<\/p>\n<div class=\"sources-expand-button-wrapper-mobile\">\n<div class=\"sources-expand-button\"><svg width=\"32\" height=\"32\" viewbox=\"0 0 32 32\" fill=\"none\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\"><path d=\"M8 12L16 20L24 12\" stroke=\"#8C9AAB\" stroke-width=\"2\" stroke-linecap=\"round\" stroke-linejoin=\"round\"><\/path><\/svg><\/div>\n<\/div>\n<\/div>\n<div class=\"sources-list-items\">\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">1.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\">Cat\u00e1logo VOKA.<\/p>\n<p><span class=\"small-text-medium text-grey\">https:\/\/catalog.voka.io\/<\/span><\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">2.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\">Luna-Ortiz, K., Reynoso-Nover\u00f3n, N., Herrera-Ponzanelli, C., Favila-Lira, S., Luna-Peteuil, Z., Herrera-Gomez, A., & Gacia-Ortega, D. Y. Sex differences according to ethnic presentation in carotid body tumors: a systematic literature review. International Journal of Otorhinolaryngology and Head and Neck Surgery. 2022 Jun;8(6):527\u2013531. DOI:10.18203\/issn.2454-5929.ijohns20221393.   <\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">3.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\">Butt N, Baek WK, Lachkar S, Iwanaga J, Mian A, Blaak C, Shah S, Griessenauer C, Tubbs RS, Loukas M. The carotid body and associated tumors: updated review with clinical\/surgical significance. Br J Neurosurg. 2019 Oct;33(5):500-503. doi: 10.1080\/02688697.2019.1617404.   <\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">4.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\">Darouassi Y, Alaoui M, Mliha Touati M, Al Maghraoui O, En-Nouali A, Bouaity B, Ammar H. Carotid Body Tumors: A Case Series and Review of the Literature. Ann Vasc Surg. 2017 Aug;43:265-271. doi: 10.1016\/j.avsg.2017.03.167.   <\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">5.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\">Gonzalez-Urquijo M, Castro-Varela A, Barrios-Ruiz A, Hinojosa-Gonzalez DE, Salas AKG, Morales EA, Gonz\u00e1lez-Gonz\u00e1lez M, Fabiani MA. Current trends in carotid body tumors: Comprehensive review. Head Neck. 2022 Oct;44(10):2316-2332. doi: 10.1002\/hed.27147.    <\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">6.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\">Ozawa H. Current management of carotid body tumors. Auris Nasus Larynx. 2024 Jun;51(3):501-506. doi: 10.1016\/j.anl.2024.01.007.   <\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">7.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\">Piazza C, Lancini D, Tomasoni M, Zafereo M, Poorten VV, Hanna E, M\u00e4kitie AA, Fernandez-Alvarez V, Kowalski LP, Chiesa-Estomba C, Ferlito A. Malignant carotid body tumors: What we know, what we do, and what we need to achieve. A systematic review of the literature. Head Neck. 2024 Mar;46(3):672-687. doi: 10.1002\/hed.27624.    <\/p>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<div class=\"sources-expand-button-wrapper\">\n<div class=\"sources-expand-button\"><svg width=\"32\" height=\"32\" viewbox=\"0 0 32 32\" fill=\"none\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\"><path d=\"M8 12L16 20L24 12\" stroke=\"#8C9AAB\" stroke-width=\"2\" stroke-linecap=\"round\" stroke-linejoin=\"round\"><\/path><\/svg><\/div>\n<\/div>\n<\/div>\n","protected":false},"excerpt":{"rendered":"<p>O paraganglioma da car\u00f3tida (quimiodectoma) \u00e9 um tumor raro, maioritariamente benigno, que surge das c\u00e9lulas quimiorreceptoras do corpo carot\u00eddeo localizado na bifurca\u00e7\u00e3o da art\u00e9ria car\u00f3tida comum. Epidemiologia A etiologia Muta\u00e7\u00f5es gen\u00e9ticas: As muta\u00e7\u00f5es nos genes que codificam as subunidades do complexo succinato desidrogenase (SDH), que est\u00e1 envolvido na cadeia respirat\u00f3ria mitocondrial e no metabolismo celular, [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":0,"template":"","diseases_category":[303],"class_list":["post-891","diseases_post","type-diseases_post","status-publish","hentry","diseases_category-vasculares"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v25.0 (Yoast SEO v26.5) - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Paraganglioma do corpo carot\u00eddeo (quimiodectoma) do pesco\u00e7o: sintomas, diagn\u00f3stico, tratamento<\/title>\n<meta name=\"description\" content=\"O paraganglioma (quimiodectoma) \u00e9 um tumor raro, predominantemente benigno, das c\u00e9lulas quimiorreceptoras na zona da bifurca\u00e7\u00e3o carot\u00eddea. 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