{"id":890,"date":"2025-05-06T16:42:17","date_gmt":"2025-05-06T13:42:17","guid":{"rendered":"https:\/\/wiki.voka.io\/diseases\/uncategorized\/rassloenie-aorty\/"},"modified":"2025-08-14T13:55:52","modified_gmt":"2025-08-14T10:55:52","slug":"dissecao-aorta","status":"publish","type":"diseases_post","link":"https:\/\/wiki.voka.io\/pt\/doencas\/vasculares\/dissecao-aorta\/","title":{"rendered":"Dissec\u00e7\u00e3o da aorta: Etiologia, patog\u00e9nese, classifica\u00e7\u00e3o, diagn\u00f3stico, m\u00e9todos de tratamento"},"content":{"rendered":"<p>A dissec\u00e7\u00e3o da aorta (dissec\u00e7\u00e3o) \u00e9 uma doen\u00e7a aguda caracterizada pela rutura da bainha interna (\u00edntima) da aorta com subsequente penetra\u00e7\u00e3o de sangue na camada m\u00e9dia (m\u00e9dia) e forma\u00e7\u00e3o de um falso l\u00famen. Esta doen\u00e7a est\u00e1 associada a um risco elevado de rutura da aorta, isqu\u00e9mia aguda de \u00f3rg\u00e3os e morte, pelo que requer um diagn\u00f3stico e tratamento urgentes. <\/p>\n<figure class=\"wp-block-image size-large\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/Vascular%20Pathology\/Aortic%20dissection%20(dissection)\/aortic%20dissection_main.webp\" alt=\"Dissec\u00e7\u00e3o da aorta ascendente com envolvimento de ramos do arco a\u00f3rtico\"><figcaption class=\"wp-element-caption\">Dissec\u00e7\u00e3o da aorta ascendente com envolvimento de ramos do arco a\u00f3rtico \u2013 <a href=\"https:\/\/catalog.voka.io\/en\/models\/6e2f9dc5-6e91-46c4-b881-b038f53acd05\/a58d9f61-f0f3-4d98-b8ed-229a62aca71b\/f83905ba-4978-4152-8555-b3408c6eb0e7\/073fd8f6-5704-47b1-af4d-3af2f8059d7b\" target=\"_blank\" rel=\"noreferrer noopener nofollow\">Modelo 3D<\/a><\/figcaption><\/figure>\n<h2 class=\"wp-block-heading\" id=\"epidemiologia\">Epidemiologia <\/h2>\n<ul class=\"wp-block-list\">\n<li>Frequ\u00eancia: 3-6 casos por 100.000 pessoas por ano. No entanto, os dados das aut\u00f3psias sugerem que a preval\u00eancia real \u00e9 mais elevada. <\/li>\n<li>G\u00e9nero: Os homens s\u00e3o mais frequentemente afectados do que as mulheres (\u2248 2:1).<\/li>\n<li>Idade: Pico aos 60-70 anos (para formas espor\u00e1dicas); formas sindr\u00f3micas (por exemplo, na s\u00edndrome de Marfan) em idades mais jovens (20-40 anos).<\/li>\n<li>Geografia\/ra\u00e7a: Os afro-americanos apresentam uma idade de in\u00edcio mais precoce e uma mortalidade mais elevada; a incid\u00eancia \u00e9 mais elevada em pa\u00edses com hipertens\u00e3o arterial mal controlada.<\/li>\n<\/ul>\n<h2 class=\"wp-block-heading\" id=\"a-etiologia\">A etiologia<\/h2>\n<ul class=\"wp-block-list\">\n<li>A hipertens\u00e3o arterial \u00e9 o principal fator (at\u00e9 80% dos casos);<\/li>\n<li>Aterosclerose: enfraquecimento da \u00edntima devido a inflama\u00e7\u00e3o e danos;<\/li>\n<li>S\u00edndromes heredit\u00e1rias do tecido conjuntivo: s\u00edndrome de Marfan (s\u00edntese de fibrilina deficiente); s\u00edndrome de Ehlers-Danlo (fraqueza do tecido conjuntivo); s\u00edndrome de Loeys-Dietz (muta\u00e7\u00f5es nos genes TGF-\u03b2);<\/li>\n<li>V\u00e1lvula a\u00f3rtica bic\u00faspide;<\/li>\n<li>Coarta\u00e7\u00e3o da aorta;<\/li>\n<li>Gravidez (especialmente no terceiro trimestre);<\/li>\n<li>Causas iatrog\u00e9nicas \u2013 cateterismos, interven\u00e7\u00f5es cir\u00fargicas;<\/li>\n<li>Traumatismo (de alta energia, mais frequentemente tor\u00e1cico);<\/li>\n<li>Doen\u00e7as inflamat\u00f3rias (vasculites) \u2013 por exemplo, arterite gigantocelular;<\/li>\n<li>Infec\u00e7\u00f5es (como a s\u00edfilis ou les\u00f5es mic\u00f3ticas).<\/li>\n<\/ul>\n<h2 class=\"wp-block-heading\" id=\"patogenese\">Patog\u00e9nese<\/h2>\n<ul class=\"wp-block-list\">\n<li>A principal liga\u00e7\u00e3o \u00e9 a rutura da \u00edntima da aorta devido a uma press\u00e3o sist\u00f3lica elevada ou a uma rutura da integridade estrutural da parede.<\/li>\n<li>Entrada de sangue na m\u00e9dia (camada m\u00e9dia) \u2192 forma\u00e7\u00e3o de um falso canal entre as camadas da parede da aorta.<\/li>\n<li>A dissemina\u00e7\u00e3o longitudinal da dissec\u00e7\u00e3o \u00e9 proximal ou distal ao local da rutura prim\u00e1ria, frequentemente envolvendo ramos da aorta.<\/li>\n<\/ul>\n<figure class=\"wp-block-image size-large\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/Vascular%20Pathology\/Aortic%20dissection%20(dissection)\/aortic%20dissection_02%20(1).webp\" alt=\"Retalho da \u00edntima descolada distal \u00e0 boca da art\u00e9ria subcl\u00e1via esquerda, l\u00famen falso e verdadeiro\"><figcaption class=\"wp-element-caption\">Retalho da \u00edntima descolada distal ao orif\u00edcio da art\u00e9ria subcl\u00e1via esquerda, l\u00famen falso e verdadeiro \u2013 <a href=\"https:\/\/catalog.voka.io\/en\/models\/6e2f9dc5-6e91-46c4-b881-b038f53acd05\/a58d9f61-f0f3-4d98-b8ed-229a62aca71b\/f83905ba-4978-4152-8555-b3408c6eb0e7\/35496f0b-8888-44ba-99c2-6c3ad11c78a7\" target=\"_blank\" rel=\"noreferrer noopener nofollow\">Modelo 3D<\/a><\/figcaption><\/figure>\n<p><strong>Poss\u00edveis consequ\u00eancias<\/strong>:<\/p>\n<ul class=\"wp-block-list\">\n<li>Compress\u00e3o do l\u00famen verdadeiro \u2192 isqu\u00e9mia dos \u00f3rg\u00e3os (rins, f\u00edgado, intestinos, membros, c\u00e9rebro).<\/li>\n<li>Se se espalhar para a raiz da aorta, pode causar insufici\u00eancia aguda da v\u00e1lvula a\u00f3rtica ou isqu\u00e9mia aguda do mioc\u00e1rdio com envolvimento dos orif\u00edcios das art\u00e9rias coron\u00e1rias.<\/li>\n<li>Rutura da camada externa (advent\u00edcia) \u2192 hemorragia maci\u00e7a da cavidade (peric\u00e1rdio, pleura, retroperitoneu).<\/li>\n<li>Forma\u00e7\u00e3o de entradas repetidas \u2013 mant\u00e9m a circula\u00e7\u00e3o no falso canal.<\/li>\n<\/ul>\n<p><strong>Marcadores de remodela\u00e7\u00e3o<\/strong>:<\/p>\n<ul class=\"wp-block-list\">\n<li>Ativa\u00e7\u00e3o de metaloproteinases (MMP-2, -9), degrada\u00e7\u00e3o do colag\u00e9nio e da elastina;<\/li>\n<li>Disfun\u00e7\u00e3o endotelial e resposta inflamat\u00f3ria (TNF-\u03b1, IL-6).<\/li>\n<\/ul>\n<h2 class=\"wp-block-heading\" id=\"classificacao-da-disseccao-da-aorta\">Classifica\u00e7\u00e3o da dissec\u00e7\u00e3o da aorta<\/h2>\n<h3 class=\"wp-block-heading\" id=\"classificacao-de-stanford\">Classifica\u00e7\u00e3o de Stanford<\/h3>\n<ul class=\"wp-block-list\">\n<li>Tipo A: afecta a aorta ascendente (com ou sem envolvimento do arco a\u00f3rtico);<\/li>\n<li>Tipo B: limita-se \u00e0 aorta descendente.<\/li>\n<\/ul>\n<p>Devido ao facto de esta classifica\u00e7\u00e3o n\u00e3o ter em conta les\u00f5es isoladas do arco a\u00f3rtico ou les\u00f5es do arco em combina\u00e7\u00e3o com a sec\u00e7\u00e3o descendente, foi proposto em 2019 o conceito de um terceiro tipo, <strong>N\u00e3o-A n\u00e3o-A e n\u00e3o-B (n\u00e3o-A n\u00e3o-B)<\/strong>.<\/p>\n<h3 class=\"wp-block-heading\" id=\"classificacao-debakey\">Classifica\u00e7\u00e3o DeBakey<\/h3>\n<ul class=\"wp-block-list\">\n<li>Tipo I: dissec\u00e7\u00e3o da aorta ascendente para o arco a\u00f3rtico ou abaixo;<\/li>\n<li>Tipo II: limita-se \u00e0 aorta ascendente;<\/li>\n<li>Tipo III: les\u00e3o apenas da aorta descendente (IIIa \u2013 at\u00e9 ao diafragma, IIIb \u2013 espalhando-se abaixo).<\/li>\n<\/ul>\n<p><a href=\"https:\/\/catalog.voka.io\/en\/models\/6e2f9dc5-6e91-46c4-b881-b038f53acd05\/a58d9f61-f0f3-4d98-b8ed-229a62aca71b\/f83905ba-4978-4152-8555-b3408c6eb0e7\/073fd8f6-5704-47b1-af4d-3af2f8059d7b\" target=\"_blank\" rel=\"noreferrer noopener nofollow\">Modelos 3D<\/a> de dissec\u00e7\u00e3o da aorta:<\/p>\n<div class=\"carousel-block\">\n<div class=\"swiper carousel-swiper carousel-swiper-block_69ecdbcf27272\">\n<div class=\"swiper-wrapper\">\n<div class=\"swiper-slide\"><img decoding=\"async\" class=\"carousel-image\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/Vascular%20Pathology\/Aortic%20dissection%20(dissection)\/aortic%20dissection_03%20(1).webp\" alt=\"Dissec\u00e7\u00e3o da aorta tipo I \"><span class=\"small-text-article text-main-text-color\">Dissec\u00e7\u00e3o da aorta tipo I <\/span><\/div>\n<div class=\"swiper-slide\"><img decoding=\"async\" class=\"carousel-image\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/Vascular%20Pathology\/Aortic%20dissection%20(dissection)\/aortic%20dissection_04%20(1).webp\" alt=\"Dissec\u00e7\u00e3o da aorta tipo II\"><span class=\"small-text-article text-main-text-color\">Dissec\u00e7\u00e3o da aorta tipo II<\/span><\/div>\n<div class=\"swiper-slide\"><img decoding=\"async\" class=\"carousel-image\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/Vascular%20Pathology\/Aortic%20dissection%20(dissection)\/aortic%20dissection_05%20(1).webp\" alt=\"Dissec\u00e7\u00e3o da aorta tipo IIIa\"><span class=\"small-text-article text-main-text-color\">Dissec\u00e7\u00e3o da aorta tipo IIIa<\/span><\/div>\n<div class=\"swiper-slide\"><img decoding=\"async\" class=\"carousel-image\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/Vascular%20Pathology\/Aortic%20dissection%20(dissection)\/aortic%20dissection_06%2B07%20(1).webp\" alt=\"Dissec\u00e7\u00e3o da aorta tipo IIIb\"><span class=\"small-text-article text-main-text-color\">Dissec\u00e7\u00e3o da aorta tipo IIIb<\/span><\/div>\n<\/div>\n<\/div>\n<div class=\"swiper-article-carousel__controls\">\n<div class=\"swiper-article-carousel__pagination-container swiper-article-carousel__pagination-container-block_69ecdbcf27272\"><\/div>\n<div class=\"swiper-article-carousel__arrows\"><button class=\"swiper__arrow swiper__arrow--prev carousel-swiper-button-prev swiper__arrow swiper__arrow--prev carousel-swiper-button-prev-block_69ecdbcf27272\"><svg xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"40\" height=\"40\" viewbox=\"0 0 40 40\" fill=\"none\"><path d=\"M20 3.75C16.7861 3.75 13.6443 4.70305 10.972 6.48862C8.29969 8.27419 6.21689 10.8121 4.98696 13.7814C3.75704 16.7507 3.43524 20.018 4.06225 23.1702C4.68926 26.3224 6.23692 29.2179 8.50952 31.4905C10.7821 33.7631 13.6776 35.3107 16.8298 35.9378C19.982 36.5648 23.2493 36.243 26.2186 35.013C29.1879 33.7831 31.7258 31.7003 33.5114 29.028C35.297 26.3557 36.25 23.2139 36.25 20C36.2455 15.6916 34.5319 11.561 31.4855 8.51454C28.439 5.46806 24.3084 3.75455 20 3.75ZM23.3844 25.3656C23.5005 25.4818 23.5926 25.6196 23.6555 25.7714C23.7184 25.9231 23.7507 26.0858 23.7507 26.25C23.7507 26.4142 23.7184 26.5769 23.6555 26.7286C23.5926 26.8804 23.5005 27.0182 23.3844 27.1344C23.2682 27.2505 23.1304 27.3426 22.9786 27.4055C22.8269 27.4683 22.6643 27.5007 22.5 27.5007C22.3358 27.5007 22.1731 27.4683 22.0214 27.4055C21.8696 27.3426 21.7318 27.2505 21.6156 27.1344L15.3656 20.8844C15.2494 20.7683 15.1572 20.6304 15.0943 20.4787C15.0314 20.3269 14.999 20.1643 14.999 20C14.999 19.8357 15.0314 19.6731 15.0943 19.5213C15.1572 19.3696 15.2494 19.2317 15.3656 19.1156L21.6156 12.8656C21.7318 12.7495 21.8696 12.6574 22.0214 12.5945C22.1731 12.5317 22.3358 12.4993 22.5 12.4993C22.6643 12.4993 22.8269 12.5317 22.9786 12.5945C23.1304 12.6574 23.2682 12.7495 23.3844 12.8656C23.5005 12.9818 23.5926 13.1196 23.6555 13.2714C23.7184 13.4231 23.7507 13.5858 23.7507 13.75C23.7507 13.9142 23.7184 14.0769 23.6555 14.2286C23.5926 14.3804 23.5005 14.5182 23.3844 14.6344L18.0172 20L23.3844 25.3656Z\" fill=\"#B5C0CD\"><\/path><\/svg><\/button><button class=\"swiper__arrow swiper__arrow--next carousel-swiper-button-next swiper__arrow swiper__arrow--next carousel-swiper-button-next-block_69ecdbcf27272\" tabindex=\"0\" aria-label=\"Next slide\"><svg xmlns=\"http:\/\/www.w3.org\/2000\/svg\" width=\"40\" height=\"40\" viewbox=\"0 0 40 40\" fill=\"none\"><path d=\"M20 3.75C16.7861 3.75 13.6443 4.70305 10.972 6.48862C8.29969 8.27419 6.21689 10.8121 4.98696 13.7814C3.75704 16.7507 3.43524 20.018 4.06225 23.1702C4.68926 26.3224 6.23692 29.2179 8.50952 31.4905C10.7821 33.7631 13.6776 35.3107 16.8298 35.9378C19.982 36.5648 23.2493 36.243 26.2186 35.013C29.1879 33.7831 31.7258 31.7003 33.5114 29.028C35.297 26.3557 36.25 23.2139 36.25 20C36.2455 15.6916 34.5319 11.561 31.4855 8.51454C28.439 5.46806 24.3084 3.75455 20 3.75ZM23.3844 25.3656C23.5005 25.4818 23.5926 25.6196 23.6555 25.7714C23.7184 25.9231 23.7507 26.0858 23.7507 26.25C23.7507 26.4142 23.7184 26.5769 23.6555 26.7286C23.5926 26.8804 23.5005 27.0182 23.3844 27.1344C23.2682 27.2505 23.1304 27.3426 22.9786 27.4055C22.8269 27.4683 22.6643 27.5007 22.5 27.5007C22.3358 27.5007 22.1731 27.4683 22.0214 27.4055C21.8696 27.3426 21.7318 27.2505 21.6156 27.1344L15.3656 20.8844C15.2494 20.7683 15.1572 20.6304 15.0943 20.4787C15.0314 20.3269 14.999 20.1643 14.999 20C14.999 19.8357 15.0314 19.6731 15.0943 19.5213C15.1572 19.3696 15.2494 19.2317 15.3656 19.1156L21.6156 12.8656C21.7318 12.7495 21.8696 12.6574 22.0214 12.5945C22.1731 12.5317 22.3358 12.4993 22.5 12.4993C22.6643 12.4993 22.8269 12.5317 22.9786 12.5945C23.1304 12.6574 23.2682 12.7495 23.3844 12.8656C23.5005 12.9818 23.5926 13.1196 23.6555 13.2714C23.7184 13.4231 23.7507 13.5858 23.7507 13.75C23.7507 13.9142 23.7184 14.0769 23.6555 14.2286C23.5926 14.3804 23.5005 14.5182 23.3844 14.6344L18.0172 20L23.3844 25.3656Z\" fill=\"#B5C0CD\"><\/path><\/svg><\/button><\/div>\n<\/div>\n<\/div>\n<p><script defer>\n    document.addEventListener('DOMContentLoaded', function() {\n        const imagesCarouselSwiper = new Swiper('.carousel-swiper-block_69ecdbcf27272', {\n            slidesPerView: 1,\n            spaceBetween: 20,\n            loop: true,\n            pagination: {\n                el: '.swiper-article-carousel__pagination-container-block_69ecdbcf27272',\n                clickable: true,\n            },\n            navigation: {\n                nextEl: '.carousel-swiper-button-next-block_69ecdbcf27272',\n                prevEl: '.carousel-swiper-button-prev-block_69ecdbcf27272',\n            },\n        })\n    })\n<\/script><\/p>\n<p><strong>Dura\u00e7\u00e3o<\/strong><\/p>\n<ul class=\"wp-block-list\">\n<li>Aguda: primeiros 14 dias ap\u00f3s o in\u00edcio da doen\u00e7a.<\/li>\n<li>Subaguda: 15 a 90 dias.<\/li>\n<li>Cr\u00f3nica: mais de 90 dias.<\/li>\n<\/ul>\n<h2 class=\"wp-block-heading\" id=\"manifestacoes-clinicas\">Manifesta\u00e7\u00f5es cl\u00ednicas<\/h2>\n<p>A sintomatologia depende da localiza\u00e7\u00e3o da dissec\u00e7\u00e3o, do grau de envolvimento dos ramos da aorta e da presen\u00e7a de complica\u00e7\u00f5es.<\/p>\n<ul class=\"wp-block-list\">\n<li><strong>Dor aguda<\/strong>: dor aguda, aguda, em \u201cpunhal\u201d, pode ser migrat\u00f3ria, a localiza\u00e7\u00e3o depende do local da dissec\u00e7\u00e3o (tipo A: dor no peito ou nas costas; tipo B: dor lombar ou abdominal).<\/li>\n<li>Hipotens\u00e3o ou choque em caso de hemorragia maci\u00e7a.<\/li>\n<li>Assimetria do pulso e da tens\u00e3o arterial nos bra\u00e7os.<\/li>\n<li>Perturba\u00e7\u00f5es neurol\u00f3gicas: fraqueza, perda de consci\u00eancia, sintomas de isqu\u00e9mia cerebral.<\/li>\n<li>Sintomas card\u00edacos: enfarte agudo do mioc\u00e1rdio (envolvimento das art\u00e9rias coron\u00e1rias), insufici\u00eancia aguda da v\u00e1lvula a\u00f3rtica.<\/li>\n<li>Insufici\u00eancia renal: fornecimento insuficiente de sangue aos rins (olig\u00faria\/an\u00faria).<\/li>\n<li>Isqu\u00e9mia intestinal: dor abdominal, diarreia com sangue.<\/li>\n<li>Tamponamento card\u00edaco com hemorragia na cavidade peric\u00e1rdica.<\/li>\n<li>Isqu\u00e9mia aguda dos membros devido a oclus\u00e3o arterial.<\/li>\n<\/ul>\n<h2 class=\"wp-block-heading\" id=\"diagnostico\">Diagn\u00f3stico<\/h2>\n<p><strong>Exame f\u00edsico<\/strong> (diferen\u00e7a de PA nas extremidades; d\u00e9fice de pulso; sopro de regurgita\u00e7\u00e3o a\u00f3rtica).<\/p>\n<p><strong>Testes de laborat\u00f3rio<\/strong>:<\/p>\n<ul class=\"wp-block-list\">\n<li>Aumento dos n\u00edveis de D-d\u00edmero nas primeiras horas; <\/li>\n<li>Biomarcadores de les\u00e3o mioc\u00e1rdica (troponina, CK-MB); <\/li>\n<li>Renal, enzimas hep\u00e1ticas, lactato \u2013 na isqu\u00e9mia de \u00f3rg\u00e3os;<\/li>\n<li>An\u00e1lises sangu\u00edneas gerais e bioqu\u00edmicas \u2013 anemia, inflama\u00e7\u00e3o.<\/li>\n<\/ul>\n<p><strong>Estudos instrumentais<\/strong>:<\/p>\n<ul class=\"wp-block-list\">\n<li><strong>Angiografia por TC<\/strong> (gold standard): elevada sensibilidade e especificidade (>95%). Dete\u00e7\u00e3o r\u00e1pida e precisa da dissec\u00e7\u00e3o, identifica\u00e7\u00e3o de condutas falsas e verdadeiras, entrada prim\u00e1ria, extens\u00e3o da dissec\u00e7\u00e3o, \u00e1reas de m\u00e1 perfus\u00e3o. <\/li>\n<li><strong>Ecografia transesof\u00e1gica<\/strong>: Alta sensibilidade, especialmente para o tipo A. Permite avaliar o flap intimal, tamanho da aorta ascendente, insufici\u00eancia a\u00f3rtica, sinais de isquemia, derrame peric\u00e1rdico.<\/li>\n<li><strong>RM<\/strong>: Alternativa \u00e0 TC na estratifica\u00e7\u00e3o cr\u00f3nica ou contra-indica\u00e7\u00f5es ao contraste. Alta sensibilidade, especialmente para avalia\u00e7\u00e3o da din\u00e2mica. <\/li>\n<\/ul>\n<h2 class=\"wp-block-heading\" id=\"tratamento-da-disseccao-da-aorta\">Tratamento da dissec\u00e7\u00e3o da aorta<\/h2>\n<h3 class=\"wp-block-heading\" id=\"tratamento-conservador-mais-comum-no-tipo-b\">Tratamento conservador (mais comum no tipo B):<\/h3>\n<p>Terapia anti-hipertensiva, antianginosa e hipolipid\u00e9mica optimizada. No per\u00edodo agudo, monitoriza\u00e7\u00e3o constante nos cuidados intensivos. <\/p>\n<ul class=\"wp-block-list\">\n<li>\u03b2-bloqueadores (esmolol, metoprolol) \u2013 primeira linha: reduzem a FC e a dp\/dt (redu\u00e7\u00e3o da for\u00e7a e da velocidade do sangue que atinge a parede).<\/li>\n<li>Nitroprussiato de s\u00f3dio, uropidil, clonidina, nitroglicerina \u2013 Redu\u00e7\u00e3o da PA (ap\u00f3s \u03b2-bloqueadores) para 100-120 mmHg. <\/li>\n<li>Morfina \u2013 analgesia e diminui\u00e7\u00e3o da ativa\u00e7\u00e3o simp\u00e1tica.<\/li>\n<\/ul>\n<p>Para dissec\u00e7\u00f5es est\u00e1veis n\u00e3o complicadas do <strong>tipo B<\/strong>:<\/p>\n<ul class=\"wp-block-list\">\n<li>Monitoriza\u00e7\u00e3o da PA e da FC;<\/li>\n<li>Acompanhamento regular (monitoriza\u00e7\u00e3o por TAC\/RM);<\/li>\n<li>Preven\u00e7\u00e3o secund\u00e1ria: anti-hipertensores, modifica\u00e7\u00e3o dos factores de risco (tabagismo, colesterol, diabetes).<\/li>\n<\/ul>\n<div class=\"social-banner-block\">\n<div class=\"social-banner-content\">\n<p class=\"h5-title text-black\">Encontra mais conte\u00fados cientificamente exactos nas nossas redes sociais<\/p>\n<p><span class=\"social-banner-text text-grey\">Subscreve e n\u00e3o percas os recursos mais recentes<\/span><\/p>\n<div class=\"social-links-wrapper\"><a class=\"social-icon-link\" href=\"https:\/\/www.facebook.com\/VOKA3DAnatomyAndPathology\/\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/facebook.svg\" alt=\"social link\"><\/a><a class=\"social-icon-link\" href=\"https:\/\/www.instagram.com\/voka.io\/\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/insta.svg\" alt=\"social link\"><\/a><a class=\"social-icon-link\" href=\"https:\/\/www.linkedin.com\/company\/voka-io\/posts\/?feedView=all\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/linkedin.svg\" alt=\"social link\"><\/a><a class=\"social-icon-link\" href=\"https:\/\/www.youtube.com\/@vokaio\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/youtube.svg\" alt=\"social link\"><\/a><a class=\"social-icon-link\" href=\"https:\/\/www.pinterest.com\/voka3danatomyandpathology\/\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/pinterest.svg\" alt=\"social link\"><\/a><a class=\"social-icon-link\" href=\"https:\/\/www.tiktok.com\/@voka.io\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/tiktok.svg\" alt=\"social link\"><\/a><a class=\"social-icon-link\" href=\"https:\/\/discord.gg\/7ejUpq8DRR\" target=\"_blank\" rel=\"nofollow noopener\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/Social%20Icons\/discord.svg\" alt=\"social link\"><\/a><\/div>\n<\/div>\n<p><img decoding=\"async\" class=\"social-banner-image\" loading=\"lazy\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/common\/social-media-banner-mobile-image.webp\" alt=\"Banner background\"><\/div>\n<h3 class=\"wp-block-heading\" id=\"tratamento-cirurgico-mais-comum-no-tipo-a\">Tratamento cir\u00fargico (mais comum no tipo A):<\/h3>\n<ol class=\"wp-block-list\">\n<li><strong>Cirurgia aberta<\/strong> (normalmente com recurso a um ventilador e a t\u00e9cnicas de hipotermia).<\/li>\n<\/ol>\n<ul class=\"wp-block-list\">\n<li>O segmento a\u00f3rtico afetado \u00e9 ressecado e a pr\u00f3tese \u00e9 suturada.<\/li>\n<li>Se o arco a\u00f3rtico estiver envolvido, as art\u00e9rias braquiocef\u00e1licas s\u00e3o reimplantadas na pr\u00f3tese (se as pr\u00f3prias art\u00e9rias braquiocef\u00e1licas estiverem envolvidas no processo de dissec\u00e7\u00e3o, tamb\u00e9m s\u00e3o pr\u00f3teses).<\/li>\n<li>Se a dissec\u00e7\u00e3o se estender \u00e0 v\u00e1lvula a\u00f3rtica, \u00e9 efectuada uma substitui\u00e7\u00e3o da v\u00e1lvula a\u00f3rtica; em alguns casos, \u00e9 poss\u00edvel uma cirurgia de preserva\u00e7\u00e3o da v\u00e1lvula.<\/li>\n<li>Se a doen\u00e7a se espalhar para os orif\u00edcios das art\u00e9rias coron\u00e1rias, pode ser feito um reimplante ou uma cirurgia de bypass aortocoron\u00e1rio.<\/li>\n<li>Quando se estende ao arco e \u00e0 sec\u00e7\u00e3o descendente, \u00e9 poss\u00edvel, em alguns casos, uma pr\u00f3tese h\u00edbrida (Frozen Elephant Trunk).<\/li>\n<\/ul>\n<ol start=\"2\" class=\"wp-block-list\">\n<li><strong>Interven\u00e7\u00e3o endovascular (TEVAR)<\/strong>: Coloca\u00e7\u00e3o de uma endopr\u00f3tese para isolar um falso l\u00famen (especialmente em caso de m\u00e1 perfus\u00e3o de \u00f3rg\u00e3os). Indicado para pacientes est\u00e1veis com complica\u00e7\u00f5es ou tipo B com hipertens\u00e3o\/dor n\u00e3o controlada e\/ou com risco de rutura. <\/li>\n<li>Em caso de rutura da aorta ou de tamponamento card\u00edaco, \u00e9 necess\u00e1ria uma interven\u00e7\u00e3o cir\u00fargica imediata.<\/li>\n<\/ol>\n<div>\n<h2 class=\"faq-title h2-article\" id=\"faq\">FAQ<\/h2>\n<div class=\"faq-section\">\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">1. Em que \u00e9 que uma dissec\u00e7\u00e3o da aorta difere de um aneurisma?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">Um aneurisma \u00e9 um alargamento da parede da aorta, e uma dissec\u00e7\u00e3o \u00e9 um rasg\u00e3o na sua camada interna onde o sangue fica preso entre as camadas da parede, criando um canal falso.  <\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">2. Quais s\u00e3o os primeiros sintomas da dissec\u00e7\u00e3o da aorta?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">O sintoma mais carater\u00edstico \u00e9 uma dor s\u00fabita e dilacerante no peito ou nas costas, frequentemente \u201cmigrat\u00f3ria\u201d. Podem ocorrer desmaios, dorm\u00eancia dos membros, falta de ar, fraqueza ou sintomas de AVC. <\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">3. Qual \u00e9 o perigo da dissec\u00e7\u00e3o da aorta?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">Trata-se de uma situa\u00e7\u00e3o de risco de vida. Sem tratamento, a mortalidade na dissec\u00e7\u00e3o da aorta ascendente (tipo A) atinge 50% nas primeiras 48 horas. A interven\u00e7\u00e3o atempada reduz significativamente os riscos.  <\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">4. Quem est\u00e1 em risco?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">Pacientes com hipertens\u00e3o arterial, s\u00edndrome de Marfan, aneurisma da aorta, casos pr\u00f3ximos de dissec\u00e7\u00e3o, mulheres gr\u00e1vidas (no terceiro trimestre), homens fumadores com mais de 60 anos de idade.<\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">5. \u00c9 necess\u00e1rio fazeres uma opera\u00e7\u00e3o?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">Se a aorta ascendente estiver envolvida (tipo A), a cirurgia \u00e9 quase sempre necess\u00e1ria. Em caso de dissec\u00e7\u00e3o da aorta descendente (tipo B), a cirurgia s\u00f3 \u00e9 necess\u00e1ria em caso de complica\u00e7\u00f5es (dor, isqu\u00e9mia, rutura, etc.).   <\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">6. Que press\u00e3o \u00e9 considerada segura?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">N\u00edvel alvo: PA sist\u00f3lica <120 mmHg, frequ\u00eancia de pulso 50-60 batimentos por minuto. Os beta-bloqueadores s\u00e3o medicamentos de primeira linha para o controlo ao longo da vida.<\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">7. Os meus familiares podem estar em risco?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">Sim, especialmente se tiveres uma doen\u00e7a heredit\u00e1ria do tecido conjuntivo (s\u00edndrome de Marfan, s\u00edndrome de Loeys-Dietz, etc.). Recomenda-se o aconselhamento gen\u00e9tico e a realiza\u00e7\u00e3o de ecografias ou TAC de rastreio de rotina aos familiares mais pr\u00f3ximos. <\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<\/div>\n<p><script type=\"application\/ld+json\">\n    {\n    \"@context\": \"https:\/\/schema.org\",\n    \"@type\": \"FAQPage\",\n    \"mainEntity\": [\n        {\n            \"@type\": \"Question\",\n            \"name\": \"Em que \u00e9 que uma dissec\u00e7\u00e3o da aorta difere de um aneurisma?\",\n            \"acceptedAnswer\": {\n                \"@type\": \"Answer\",\n                \"text\": \"Um aneurisma \u00e9 um alargamento da parede da aorta, e uma dissec\u00e7\u00e3o \u00e9 um rasg\u00e3o na sua camada interna onde o sangue fica preso entre as camadas da parede, criando um canal falso.  \"\n            }\n        },\n        {\n            \"@type\": \"Question\",\n            \"name\": \"Quais s\u00e3o os primeiros sintomas da dissec\u00e7\u00e3o da aorta?\",\n            \"acceptedAnswer\": {\n                \"@type\": \"Answer\",\n                \"text\": \"O sintoma mais carater\u00edstico \u00e9 uma dor s\u00fabita e dilacerante no peito ou nas costas, frequentemente \\\"migrat\u00f3ria\\\". Podem ocorrer desmaios, dorm\u00eancia dos membros, falta de ar, fraqueza ou sintomas de AVC. \"\n            }\n        },\n        {\n            \"@type\": \"Question\",\n            \"name\": \"Qual \u00e9 o perigo da dissec\u00e7\u00e3o da aorta?\",\n            \"acceptedAnswer\": {\n                \"@type\": \"Answer\",\n                \"text\": \"Trata-se de uma situa\u00e7\u00e3o de risco de vida. Sem tratamento, a mortalidade na dissec\u00e7\u00e3o da aorta ascendente (tipo A) atinge 50% nas primeiras 48 horas. A interven\u00e7\u00e3o atempada reduz significativamente os riscos.  \"\n            }\n        },\n        {\n            \"@type\": \"Question\",\n            \"name\": \"Quem est\u00e1 em risco?\",\n            \"acceptedAnswer\": {\n                \"@type\": \"Answer\",\n                \"text\": \"Pacientes com hipertens\u00e3o arterial, s\u00edndrome de Marfan, aneurisma da aorta, casos pr\u00f3ximos de dissec\u00e7\u00e3o, mulheres gr\u00e1vidas (no terceiro trimestre), homens fumadores com mais de 60 anos de idade.\"\n            }\n        },\n        {\n            \"@type\": \"Question\",\n            \"name\": \"\u00c9 necess\u00e1rio fazeres uma opera\u00e7\u00e3o?\",\n            \"acceptedAnswer\": {\n                \"@type\": \"Answer\",\n                \"text\": \"Se a aorta ascendente estiver envolvida (tipo A), a cirurgia \u00e9 quase sempre necess\u00e1ria. Em caso de dissec\u00e7\u00e3o da aorta descendente (tipo B), a cirurgia s\u00f3 \u00e9 necess\u00e1ria em caso de complica\u00e7\u00f5es (dor, isqu\u00e9mia, rutura, etc.).   \"\n            }\n        },\n        {\n            \"@type\": \"Question\",\n            \"name\": \"Que press\u00e3o \u00e9 considerada segura?\",\n            \"acceptedAnswer\": {\n                \"@type\": \"Answer\",\n                \"text\": \"N\u00edvel alvo: PA sist\u00f3lica <120 mmHg, frequ\u00eancia de pulso 50-60 batimentos por minuto. Os beta-bloqueadores s\u00e3o medicamentos de primeira linha para o controlo ao longo da vida.\"\n            }\n        },\n        {\n            \"@type\": \"Question\",\n            \"name\": \"Os meus familiares podem estar em risco?\",\n            \"acceptedAnswer\": {\n                \"@type\": \"Answer\",\n                \"text\": \"Sim, especialmente se tiveres uma doen\u00e7a heredit\u00e1ria do tecido conjuntivo (s\u00edndrome de Marfan, s\u00edndrome de Loeys-Dietz, etc.). Recomenda-se o aconselhamento gen\u00e9tico e a realiza\u00e7\u00e3o de ecografias ou TAC de rastreio de rotina aos familiares mais pr\u00f3ximos. \"\n            }\n        }\n    ]\n}<\/script><\/div>\n<div class=\"sources-list-block sources-list-hidden\" id=\"lista-de-fontes\">\n<div class=\"sources-list-content\">\n<div class=\"sources-list-title\">\n<p class=\"small-text-bold text-black sources-list-title-text\">Lista de fontes<\/p>\n<div class=\"sources-expand-button-wrapper-mobile\">\n<div class=\"sources-expand-button\"><svg width=\"32\" height=\"32\" viewbox=\"0 0 32 32\" fill=\"none\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\"><path d=\"M8 12L16 20L24 12\" stroke=\"#8C9AAB\" stroke-width=\"2\" stroke-linecap=\"round\" stroke-linejoin=\"round\"><\/path><\/svg><\/div>\n<\/div>\n<\/div>\n<div class=\"sources-list-items\">\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">1.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\">Cat\u00e1logo VOKA.<\/p>\n<p><span class=\"small-text-medium text-grey\">https:\/\/catalog.voka.io\/<\/span><\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">2.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\">Reed MJ. Diagnosis and management of acute aortic dissection in the emergency department. Br J Hosp Med (Lond). 2024 Apr 30;85(4):1-9. doi: 10.12968\/hmed.2023.0366.    <\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">3.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\">Hameed I, Cifu AS, Vallabhajosyula P. Management of Thoracic Aortic Dissection. JAMA. 2023 Mar 7;329(9):756-757. doi: 10.1001\/jama.2023.0265.   <\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">4.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\">Tchana-Sato V, Sakalihasan N, Defraigne JO. Aortic dissection. Rev Med Liege. 2018 May;73(5-6):290-295.   <\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">5.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\">JCS\/JSCVS\/JATS\/JSVS 2020 Guideline on Diagnosis and Treatment of Aortic Aneurysm and Aortic Dissection. Circ J. 2023 Sep 25;87(10):1410-1621. doi: 10.1253\/circj.CJ-22-0794.  <\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">6.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\">Zeng T, Shi L, Ji Q, Shi Y, Huang Y, Liu Y, Gan J, Yuan J, Lu Z, Xue Y, Hu H, Liu L, Lin Y. Cytokines in aortic dissection. Clin Chim Acta. 2018 Nov;486:177-182. doi: 10.1016\/j.cca.2018.08.005.   <\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">7.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\">Khaja MS, Williams DM. Aortic Dissection: Introduction. Tech Vasc Interv Radiol. 2021 Jun;24(2):100745. doi: 10.1016\/j.tvir.2021.100745.    <\/p>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<div class=\"sources-expand-button-wrapper\">\n<div class=\"sources-expand-button\"><svg width=\"32\" height=\"32\" viewbox=\"0 0 32 32\" fill=\"none\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\"><path d=\"M8 12L16 20L24 12\" stroke=\"#8C9AAB\" stroke-width=\"2\" stroke-linecap=\"round\" stroke-linejoin=\"round\"><\/path><\/svg><\/div>\n<\/div>\n<\/div>\n","protected":false},"excerpt":{"rendered":"<p>A dissec\u00e7\u00e3o da aorta (dissec\u00e7\u00e3o) \u00e9 uma doen\u00e7a aguda caracterizada pela rutura da bainha interna (\u00edntima) da aorta com subsequente penetra\u00e7\u00e3o de sangue na camada m\u00e9dia (m\u00e9dia) e forma\u00e7\u00e3o de um falso l\u00famen. Esta doen\u00e7a est\u00e1 associada a um risco elevado de rutura da aorta, isqu\u00e9mia aguda de \u00f3rg\u00e3os e morte, pelo que requer um [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":0,"template":"","diseases_category":[303],"class_list":["post-890","diseases_post","type-diseases_post","status-publish","hentry","diseases_category-vasculares"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v25.0 (Yoast SEO v26.5) - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Dissec\u00e7\u00e3o da aorta (dissec\u00e7\u00e3o): O que \u00e9, sintomas, causas, classifica\u00e7\u00e3o, tratamento<\/title>\n<meta name=\"description\" content=\"A dissec\u00e7\u00e3o da aorta (dissec\u00e7\u00e3o) \u00e9 uma doen\u00e7a em que a parede interna da aorta se rompe, com o sangue a fluir entre as suas camadas e a criar um canal falso. 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