{"id":622,"date":"2025-05-27T19:45:27","date_gmt":"2025-05-27T16:45:27","guid":{"rendered":"https:\/\/wiki.voka.io\/diseases\/uncategorized\/artere-sous-claviere-aberrante\/"},"modified":"2025-11-05T15:28:18","modified_gmt":"2025-11-05T12:28:18","slug":"artere-sous-claviere-aberrante","status":"publish","type":"diseases_post","link":"https:\/\/wiki.voka.io\/fr\/maladies\/systeme-vasculaire\/artere-sous-claviere-aberrante\/","title":{"rendered":"Art\u00e8re subclavi\u00e8re aberrante : \u00e9tiologie, pathog\u00e9nie, classification, diagnostic et traitement"},"content":{"rendered":"<p>L\u2019<strong>art\u00e8re subclavi\u00e8re droite aberrante (ASDA)<\/strong> est l\u2019anomalie la plus fr\u00e9quente de la crosse aortique, touchant environ 0,5 \u00e0 2 % de la population. Dans la grande majorit\u00e9 des cas, il s\u2019agit de l\u2019art\u00e8re subclavi\u00e8re droite aberrante (<g id=\"gid_1\">arteria lusoria<\/g>). L\u2019anomalie peut \u00eatre d\u00e9tect\u00e9e \u00e0 tout \u00e2ge, mais le plus souvent, elle est diagnostiqu\u00e9e soit dans l\u2019enfance en pr\u00e9sence de sympt\u00f4mes, soit fortuitement chez l\u2019adulte \u00e0 l\u2019occasion d\u2019examens d\u2019imagerie.  <\/p>\n<figure class=\"wp-block-image size-large\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/Vascular%20Pathology\/Aberrant%20subclavian%20artery\/Aberrantnaya_pravaya_podklyuchichnaya_arteriya_1.webp\" alt=\"Art\u00e8re subclavi\u00e8re droite aberrante en association avec un tronc bicarotidien (les art\u00e8res carotides communes gauche et droite forment un seul tronc \u00e0 partir de la crosse aortique)\"><figcaption class=\"wp-element-caption\">Art\u00e8re subclavi\u00e8re droite aberrante en association avec un tronc bicarotidien (les art\u00e8res carotides communes gauche et droite forment un seul tronc \u00e0 partir de la crosse aortique) \u2013 <a href=\"https:\/\/catalog.voka.io\/en\/models\/6e2f9dc5-6e91-46c4-b881-b038f53acd05\/0b4c0e8d-91d8-429b-9f93-d5514f0c87da\/8ee57cc4-c544-40ef-bd75-326559e090bb\/ec2c8240-ef5c-4aaf-b79c-8255a97e7adb\" target=\"_blank\" rel=\"noreferrer noopener nofollow\">Mod\u00e8le 3D<\/a><\/figcaption><\/figure>\n<h2 class=\"wp-block-heading\" id=\"etiologie\">\u00c9tiologie<\/h2>\n<p>L\u2019ASDA est le r\u00e9sultat d\u2019un d\u00e9veloppement embryologique anormal des <strong>4e et 7e arcs aortiques<\/strong>. Sa cause principale est la pr\u00e9servation du 7e arc aortique droit avec la r\u00e9gression du 4e arc droit, ce qui a pour cons\u00e9quence que l\u2019art\u00e8re subclavi\u00e8re droite prend naissance de l\u2019aorte distale, le plus souvent apr\u00e8s l\u2019art\u00e8re subclavi\u00e8re gauche, et passe derri\u00e8re l\u2019\u0153sophage. <\/p>\n<p><strong>Facteurs de risque :<\/strong><\/p>\n<ul class=\"wp-block-list\">\n<li>Anomalies g\u00e9n\u00e9tiques (par exemple, d\u00e9l\u00e9tion 22q11.2) ;<\/li>\n<li>Syndromes avec d\u00e9veloppement vasculaire anormal (de Di George, de Turner) ;<\/li>\n<li>Association fr\u00e9quente avec des cardiopathies cong\u00e9nitales (t\u00e9tralogie de Fallot, transposition des gros vaisseaux) ;<\/li>\n<li>Possible pr\u00e9disposition h\u00e9r\u00e9ditaire, surtout en pr\u00e9sence d\u2019une anomalie similaire chez des parents du premier degr\u00e9.<\/li>\n<\/ul>\n<figure class=\"wp-block-video\" id=\"animation-3d-artere-sous-claviere-droite-aberrante-combinee-au-tronc-bicarotidien\"><video controls><source data-src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/Vascular%20Pathology\/Aberrant%20subclavian%20artery\/aberrant-right-subclavian-artery-with-bicarotid-trunk.webm\" type=\"video\/webm\"><\/source><\/video><figcaption class=\"wp-element-caption\">Animation 3D \u2013 art\u00e8re sous-clavi\u00e8re droite aberrante combin\u00e9e au tronc bicarotidien<\/figcaption><\/figure>\n<h2 class=\"wp-block-heading\" id=\"pathogenie\">Pathog\u00e9nie<\/h2>\n<p>L\u2019art\u00e8re subclavi\u00e8re droite aberrante peut entra\u00eener une compression des structures voisines.<\/p>\n<ol class=\"wp-block-list\">\n<li>Lorsque l\u2019art\u00e8re provoque la compression de l\u2019\u0153sophage, une <strong>dysphagie<\/strong> peut appara\u00eetre.<\/li>\n<li>En cas de compression s\u00e9v\u00e8re de la trach\u00e9e, des <strong>sympt\u00f4mes respiratoires<\/strong> surviennent (toux, dyspn\u00e9e, stridor).<\/li>\n<li>Dans de rares cas, un <strong>anneau art\u00e9riel<\/strong> peut se former (surtout en cas de persistance de la crosse aortique droite et du canal art\u00e9riel).<\/li>\n<li>Une dilatation an\u00e9vrysmale du vaisseau aberrant (diverticule de Kommerell) pr\u00e9sente un risque de rupture ou de thrombose.<\/li>\n<\/ol>\n<figure class=\"wp-block-image size-large\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/Vascular%20Pathology\/Aberrant%20subclavian%20artery\/Aberrantnaya_pravaya_podklyuchichnaya_arteriya_2.webp\" alt=\"En passant derri\u00e8re l'\u0153sophage, l'art\u00e8re subclavi\u00e8re droite aberrante entra\u00eene sa compression\"><figcaption class=\"wp-element-caption\">En passant derri\u00e8re l\u2019\u0153sophage, l\u2019art\u00e8re subclavi\u00e8re droite aberrante entra\u00eene sa compression<\/figcaption><\/figure>\n<h2 class=\"wp-block-heading\" id=\"classification\">Classification<\/h2>\n<figure class=\"wp-block-table table-to-cards table-accents\">\n<table class=\"has-fixed-layout\">\n<tbody>\n<tr>\n<td class=\"has-text-align-center\" data-align=\"center\"><strong>Selon le trajet de l\u2019art\u00e8re par rapport \u00e0 la trach\u00e9e et \u00e0 l\u2019\u0153sophage : <\/strong><br \/>R\u00e9tro-\u0153sophagienne<\/td>\n<td>Derri\u00e8re l\u2019\u0153sophage (85 % des cas)<\/td>\n<\/tr>\n<tr>\n<td class=\"has-text-align-center\" data-align=\"center\">Trach\u00e9o-\u0153sophagienne<\/td>\n<td>Entre la trach\u00e9e et l\u2019\u0153sophage (10\u201315 % des cas)<\/td>\n<\/tr>\n<tr>\n<td class=\"has-text-align-center\" data-align=\"center\">Pr\u00e9trach\u00e9ale<\/td>\n<td>Devant la trach\u00e9e (moins de 5 % des cas)<\/td>\n<\/tr>\n<tr>\n<td class=\"has-text-align-center\" data-align=\"center\"><strong>Par la pr\u00e9sence d\u2019un an\u00e9vrysme \u00e0 l\u2019orifice de l\u2019art\u00e8re (diverticule de Kommerell) : <\/strong><br \/>Sans diverticule<\/td>\n<td>Souvent asymptomatique<\/td>\n<\/tr>\n<tr>\n<td class=\"has-text-align-center\" data-align=\"center\">Avec diverticule de Kommerell<\/td>\n<td>L\u2019orifice de l\u2019ASDA est dilat\u00e9 de mani\u00e8re an\u00e9vrysmale. Risque accru de rupture, de thrombose, de dysphagie <\/td>\n<\/tr>\n<tr>\n<td class=\"has-text-align-center\" data-align=\"center\"><strong>Selon le type de crosse aortique : <\/strong><br \/>Crosse aortique gauche<\/td>\n<td>Position normale de la crosse. L\u2019ASDA est le dernier vaisseau (type le plus fr\u00e9quent)<\/td>\n<\/tr>\n<tr>\n<td class=\"has-text-align-center\" data-align=\"center\">Crosse aortique droite<\/td>\n<td>L\u2019ASDA est le premier vaisseau \u2192 Risque accru de formation d\u2019un anneau vasculaire<\/td>\n<\/tr>\n<tr>\n<td class=\"has-text-align-center\" data-align=\"center\">Double crosse aortique<\/td>\n<td>Les deux crosses sont pr\u00e9serv\u00e9es, formant un anneau art\u00e9riel<\/td>\n<\/tr>\n<tr>\n<td class=\"has-text-align-center\" data-align=\"center\"><strong>Selon la pr\u00e9sence d\u2019un anneau vasculaire : <\/strong><br \/>Sans anneau<\/td>\n<td>Plus souvent asymptomatique<\/td>\n<\/tr>\n<tr>\n<td class=\"has-text-align-center\" data-align=\"center\">Anneau partiel<\/td>\n<td>En pr\u00e9sence d\u2019un canal art\u00e9riel mais sans boucle compl\u00e8te (avec ou sans sympt\u00f4mes)<\/td>\n<\/tr>\n<tr>\n<td class=\"has-text-align-center\" data-align=\"center\">Anneau art\u00e9riel complet<\/td>\n<td>Association avec un canal art\u00e9riel persistant et une crosse droite. Compression trach\u00e9ale et \u0153sophagienne. Indication chirurgicale <\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n<\/figure>\n<figure class=\"wp-block-image size-large\"><img decoding=\"async\" src=\"https:\/\/storage.googleapis.com\/dev_wiki_voka_io_303011\/articles\/Vascular%20Pathology\/Aberrant%20subclavian%20artery\/Aberrantnaya_pravaya_podklyuchichnaya_arteriya_3.webp\" alt=\"Dans ce cas : type r\u00e9tro-\u0153sophagien, sans diverticule, crosse aortique gauche, sans anneau art\u00e9riel\"><figcaption class=\"wp-element-caption\">Dans ce cas : type r\u00e9tro-\u0153sophagien, sans diverticule, crosse aortique gauche, sans anneau art\u00e9riel<\/figcaption><\/figure>\n<h2 class=\"wp-block-heading\" id=\"manifestations-cliniques\">Manifestations cliniques<\/h2>\n<p>Chez la plupart des patients adultes, l\u2019ASDA est asymptomatique. Les sympt\u00f4mes sont plus fr\u00e9quents chez les enfants, surtout en cas d\u2019anomalies combin\u00e9es. <\/p>\n<p>Principales manifestations cliniques<strong> :<\/strong><\/p>\n<ul class=\"wp-block-list\">\n<li><strong>Dysphagie <\/strong>(trouble de la d\u00e9glutition, le plus souvent d\u2019aliments durs) \u2013 le principal sympt\u00f4me chez l\u2019adulte ;<\/li>\n<li><strong>Dyspn\u00e9e, toux, respiration sifflante<\/strong> \u2013 en cas de compression trach\u00e9ale ;<\/li>\n<li><strong>Infections r\u00e9currentes des voies respiratoires<\/strong> \u2013 chez l\u2019enfant ;<\/li>\n<li><strong>Douleur thoracique, enrouement, syndrome de Horner <\/strong>\u2013 en cas de compression des structures neurovasculaires voisines ;<\/li>\n<li>Les sympt\u00f4mes peuvent s\u2019aggraver en cas de dilatation an\u00e9vrysmale du vaisseau.<\/li>\n<\/ul>\n<h2 class=\"wp-block-heading\" id=\"diagnostic\">Diagnostic<\/h2>\n<p>L\u2019approche diagnostique d\u00e9pend de la gravit\u00e9 des sympt\u00f4mes et de la pr\u00e9sence d\u2019anomalies associ\u00e9es. Les techniques modernes permettent de visualiser la pathologie avec une grande pr\u00e9cision. <\/p>\n<ul class=\"wp-block-list\">\n<li><strong><span class=\"glossary-term\" data-title=\"Tomodensitom\u00e9trie\" data-tooltip=\"La tomodensitom\u00e9trie est une technique de radiodiagnostic qui utilise des rayons X pour obtenir des images en coupe des organes et des tissus internes. C&#039;est une des m\u00e9thodes d&#039;imagerie principales de la m\u00e9decine moderne, caract\u00e9ris\u00e9e par une grande capacit\u00e9 d&#039;information.\" data-link=\"https:\/\/wiki.voka.io\/fr\/glossaire\/tdm-tomodensitometrie\/\">Angio-TDM<\/span> (\u00e9talon-or) : <\/strong>visualisation de l\u2019anatomie de la crosse aortique, confirmation de l\u2019aberration, \u00e9valuation de la compression. <\/li>\n<li><strong>Angio-IRM : <\/strong>alternative \u00e0 la TDM en cas de contre-indication \u00e0 l\u2019iode. <\/li>\n<li><strong>Radiographie de l\u2019\u0153sophage avec baryum :<\/strong> indiqu\u00e9e en cas de dysphagie. Une d\u00e9formation de la paroi post\u00e9rieure de l\u2019\u0153sophage est un signe typique.  <\/li>\n<li><strong>Bronchofibroscopie :<\/strong> en cas de sympt\u00f4mes respiratoires. Diagnostic d\u2019une compression trach\u00e9ale.  <\/li>\n<li><strong>\u00c9chocardiographie :<\/strong> \u00e9valuation des malformations cardiaques associ\u00e9es. Visualisation de l\u2019art\u00e8re anormale, \u00e9valuation du flux sanguin.  <\/li>\n<\/ul>\n<h2 class=\"wp-block-heading\" id=\"traitement-de-l-artere-subclaviere-aberrante\">Traitement de l\u2019art\u00e8re subclavi\u00e8re aberrante<\/h2>\n<h3 class=\"wp-block-heading\" id=\"traitement-conservateur\">Traitement conservateur<\/h3>\n<ul class=\"wp-block-list\">\n<li>Exclusion des facteurs qui aggravent la dysphagie (par exemple, aliments durs ou secs).<\/li>\n<li>Surveillance par imagerie en cas d\u2019\u00e9volution asymptomatique.<\/li>\n<li>En pr\u00e9sence d\u2019un spasme \u0153sophagien ou d\u2019une inflammation de l\u2019\u0153sophage, il est possible d\u2019utiliser les m\u00e9dicaments suivants :\n<ul class=\"wp-block-list\">\n<li>Prokin\u00e9tiques (avant la prescription, il est n\u00e9cessaire d\u2019exclure une obstruction s\u00e9v\u00e8re, par exemple un diverticule de Kommerell avec compression importante) ;<\/li>\n<li>Inhibiteurs de la pompe \u00e0 protons (en cas de pr\u00e9sence ou de suspicion de reflux gastro-\u0153sophagien ou d\u2019\u0153sophagite concomitants).<\/li>\n<\/ul>\n<\/li>\n<\/ul>\n<h3 class=\"wp-block-heading\" id=\"traitement-chirurgical\">Traitement chirurgical<\/h3>\n<p><strong>Indications<\/strong> :<\/p>\n<ul class=\"wp-block-list\">\n<li>Dysphagie symptomatique ou obstruction respiratoire ;<\/li>\n<li>An\u00e9vrysme du diverticule de Kommerell ;<\/li>\n<li>Association avec d\u2019autres malformations cardiaques n\u00e9cessitant une correction.<\/li>\n<\/ul>\n<p><strong>M\u00e9thodes :<\/strong><\/p>\n<p><strong>Ligature et r\u00e9implantation de l\u2019art\u00e8re<\/strong> dans l\u2019art\u00e8re carotide commune droite ou dans l\u2019art\u00e8re du tronc brachio-c\u00e9phalique (par acc\u00e8s supraclaviculaire ou thoracotomie lat\u00e9rale).<\/p>\n<p><strong>R\u00e9section du diverticule de Kommerell<\/strong><\/p>\n<ul class=\"wp-block-list\">\n<li>Ablation du segment an\u00e9vrysmal, souvent combin\u00e9e \u00e0 la r\u00e9implantation de l\u2019art\u00e8re.<\/li>\n<li>La thoracotomie est \u00e0 privil\u00e9gier.<\/li>\n<li>Chez les personnes \u00e2g\u00e9es pr\u00e9sentant une calcinose\/thrombose importante du diverticule de Kommerell, il est pr\u00e9f\u00e9rable d\u2019utiliser un stent-greffe ou des approches hybrides.<\/li>\n<\/ul>\n<p><strong>Interventions hybrides : <\/strong>utilisation de stent-greffes avec r\u00e9implantation pr\u00e9alable de l\u2019art\u00e8re subclavi\u00e8re aberrante dans l\u2019art\u00e8re carotide.<\/p>\n<div>\n<h2 class=\"faq-title h2-article\" id=\"faq\">FAQ<\/h2>\n<div class=\"faq-section\">\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">1. Qu\u2019est-ce qu\u2019une art\u00e8re subclavi\u00e8re droite aberrante ?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">Il s\u2019agit d\u2019une anomalie dans laquelle l\u2019art\u00e8re subclavi\u00e8re droite provient de l\u2019aorte \u00e0 un endroit atypique et passe derri\u00e8re l\u2019\u0153sophage, provoquant parfois une compression \u0153sophagienne.<\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">2. Quelle est la fr\u00e9quence d\u2019une art\u00e8re subclavi\u00e8re droite aberrante ?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">C\u2019est l\u2019anomalie isol\u00e9e la plus fr\u00e9quente de la crosse aortique, qui touche environ 0,5 \u00e0 2 % de la population. <\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">3. Quels sont les sympt\u00f4mes d\u2019une art\u00e8re subclavi\u00e8re droite aberrante ?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">Le sympt\u00f4me le plus courant est la dysphagie (difficult\u00e9 \u00e0 avaler). La toux, la respiration sifflante, les infections respiratoires r\u00e9currentes, en particulier chez les enfants, sont \u00e9galement possibles. <\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">4. Comment le diagnostic est-il confirm\u00e9 ?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">L\u2019angio-TDM est la m\u00e9thode la plus pr\u00e9cise pour visualiser le trajet de l\u2019art\u00e8re et son effet sur l\u2019\u0153sophage\/la trach\u00e9e. Les options suppl\u00e9mentaires sont la radiographie de l\u2019\u0153sophage avec baryum et l\u2019IRM. <\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">5. Une art\u00e8re aberrante met-elle la vie en danger ?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">Dans la plupart des cas, non. Mais en pr\u00e9sence d\u2019une dilatation an\u00e9vrysmale (diverticule de Kommerell), le risque de thrombose, de rupture ou d\u2019embolie peut survenir. <\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">6. Cette anomalie doit-elle toujours \u00eatre op\u00e9r\u00e9e ?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">Non. Le traitement chirurgical n\u2019est indiqu\u00e9 qu\u2019en cas de sympt\u00f4mes graves, d\u2019an\u00e9vrysme ou de pr\u00e9sence d\u2019un anneau art\u00e9riel entra\u00eenant une compression. <\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">7. Est-il possible de g\u00e9rer les sympt\u00f4mes sans chirurgie ?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">Dans les cas l\u00e9gers, oui. Les mesures \u00e0 prendre sont : corrections di\u00e9t\u00e9tiques, inhibiteurs de la pompe \u00e0 protons, prokin\u00e9tiques, traitement d\u2019une \u0153sophagite concomitante. <\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">8. Qu\u2019est-ce qu\u2019un diverticule de Kommerell ?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">Il s\u2019agit d\u2019une dilatation sacciforme \u00e0 l\u2019endroit o\u00f9 l\u2019art\u00e8re aberrante na\u00eet de l\u2019aorte. Elle peut \u00eatre \u00e0 l\u2019origine de sympt\u00f4mes ou pr\u00e9senter un risque chirurgical. <\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<div class=\"faq-item faq-answer-hidden\">\n<div class=\"question-block\">\n<div class=\"faq-question\">\n<p class=\" text-black h5-title\">9. Quelles sont les cons\u00e9quences d\u2019une art\u00e8re subclavi\u00e8re droite aberrante chez le f\u0153tus ?<\/p>\n<\/div>\n<div class=\"faq-answer text-main-text-color main-text-medium\">Les cons\u00e9quences d\u2019une art\u00e8re subclavi\u00e8re droite aberrante chez le f\u0153tus sont g\u00e9n\u00e9ralement li\u00e9es \u00e0 une possible compression de l\u2019\u0153sophage, qui peut entra\u00eener des troubles de la d\u00e9glutition et du transfert des aliments vers l\u2019estomac. Dans la plupart des cas, l\u2019anomalie est asymptomatique et n\u2019affecte pas consid\u00e9rablement le d\u00e9veloppement du f\u0153tus. Mais en cas de compression s\u00e9v\u00e8re ou de complications telles qu\u2019une dilatation an\u00e9vrysmale, des probl\u00e8mes plus graves peuvent survenir, n\u00e9cessitant une surveillance et, dans de rares cas, une intervention apr\u00e8s la naissance.  <\/div>\n<\/div>\n<div class=\"expand-button-wrapper\"><button class=\"text-accent expand-button\">+<\/button><\/div>\n<\/div>\n<\/div>\n<p><script type=\"application\/ld+json\">\n    {\n    \"@context\": \"https:\/\/schema.org\",\n    \"@type\": \"FAQPage\",\n    \"mainEntity\": [\n        {\n            \"@type\": \"Question\",\n            \"name\": \"Qu'est-ce qu'une art\u00e8re subclavi\u00e8re droite aberrante ?\",\n            \"acceptedAnswer\": {\n                \"@type\": \"Answer\",\n                \"text\": \"Il s'agit d'une anomalie dans laquelle l'art\u00e8re subclavi\u00e8re droite provient de l'aorte \u00e0 un endroit atypique et passe derri\u00e8re l'\u0153sophage, provoquant parfois une compression \u0153sophagienne.\"\n            }\n        },\n        {\n            \"@type\": \"Question\",\n            \"name\": \"Quelle est la fr\u00e9quence d'une art\u00e8re subclavi\u00e8re droite aberrante ?\",\n            \"acceptedAnswer\": {\n                \"@type\": \"Answer\",\n                \"text\": \"C'est l'anomalie isol\u00e9e la plus fr\u00e9quente de la crosse aortique, qui touche environ 0,5 \u00e0 2 % de la population. \"\n            }\n        },\n        {\n            \"@type\": \"Question\",\n            \"name\": \"Quels sont les sympt\u00f4mes d'une art\u00e8re subclavi\u00e8re droite aberrante ?\",\n            \"acceptedAnswer\": {\n                \"@type\": \"Answer\",\n                \"text\": \"Le sympt\u00f4me le plus courant est la dysphagie (difficult\u00e9 \u00e0 avaler). La toux, la respiration sifflante, les infections respiratoires r\u00e9currentes, en particulier chez les enfants, sont \u00e9galement possibles. \"\n            }\n        },\n        {\n            \"@type\": \"Question\",\n            \"name\": \"Comment le diagnostic est-il confirm\u00e9 ?\",\n            \"acceptedAnswer\": {\n                \"@type\": \"Answer\",\n                \"text\": \"L'angio-TDM est la m\u00e9thode la plus pr\u00e9cise pour visualiser le trajet de l'art\u00e8re et son effet sur l'\u0153sophage\/la trach\u00e9e. Les options suppl\u00e9mentaires sont la radiographie de l'\u0153sophage avec baryum et l'IRM. \"\n            }\n        },\n        {\n            \"@type\": \"Question\",\n            \"name\": \"Une art\u00e8re aberrante met-elle la vie en danger ?\",\n            \"acceptedAnswer\": {\n                \"@type\": \"Answer\",\n                \"text\": \"Dans la plupart des cas, non. Mais en pr\u00e9sence d'une dilatation an\u00e9vrysmale (diverticule de Kommerell), le risque de thrombose, de rupture ou d'embolie peut survenir. \"\n            }\n        },\n        {\n            \"@type\": \"Question\",\n            \"name\": \"Cette anomalie doit-elle toujours \u00eatre op\u00e9r\u00e9e ?\",\n            \"acceptedAnswer\": {\n                \"@type\": \"Answer\",\n                \"text\": \"Non. Le traitement chirurgical n'est indiqu\u00e9 qu'en cas de sympt\u00f4mes graves, d'an\u00e9vrysme ou de pr\u00e9sence d'un anneau art\u00e9riel entra\u00eenant une compression. \"\n            }\n        },\n        {\n            \"@type\": \"Question\",\n            \"name\": \"Est-il possible de g\u00e9rer les sympt\u00f4mes sans chirurgie ?\",\n            \"acceptedAnswer\": {\n                \"@type\": \"Answer\",\n                \"text\": \"Dans les cas l\u00e9gers, oui. Les mesures \u00e0 prendre sont : corrections di\u00e9t\u00e9tiques, inhibiteurs de la pompe \u00e0 protons, prokin\u00e9tiques, traitement d'une \u0153sophagite concomitante. \"\n            }\n        },\n        {\n            \"@type\": \"Question\",\n            \"name\": \"Qu'est-ce qu'un diverticule de Kommerell ?\",\n            \"acceptedAnswer\": {\n                \"@type\": \"Answer\",\n                \"text\": \"Il s'agit d'une dilatation sacciforme \u00e0 l'endroit o\u00f9 l'art\u00e8re aberrante na\u00eet de l'aorte. Elle peut \u00eatre \u00e0 l'origine de sympt\u00f4mes ou pr\u00e9senter un risque chirurgical. \"\n            }\n        },\n        {\n            \"@type\": \"Question\",\n            \"name\": \"Quelles sont les cons\u00e9quences d'une art\u00e8re subclavi\u00e8re droite aberrante chez le f\u0153tus ?\",\n            \"acceptedAnswer\": {\n                \"@type\": \"Answer\",\n                \"text\": \"Les cons\u00e9quences d'une art\u00e8re subclavi\u00e8re droite aberrante chez le f\u0153tus sont g\u00e9n\u00e9ralement li\u00e9es \u00e0 une possible compression de l'\u0153sophage, qui peut entra\u00eener des troubles de la d\u00e9glutition et du transfert des aliments vers l\u2019estomac. Dans la plupart des cas, l'anomalie est asymptomatique et n'affecte pas consid\u00e9rablement le d\u00e9veloppement du f\u0153tus. Mais en cas de compression s\u00e9v\u00e8re ou de complications telles qu'une dilatation an\u00e9vrysmale, des probl\u00e8mes plus graves peuvent survenir, n\u00e9cessitant une surveillance et, dans de rares cas, une intervention apr\u00e8s la naissance.  \"\n            }\n        }\n    ]\n}<\/script><\/div>\n<div class=\"sources-list-block sources-list-hidden\" id=\"liste-des-sources\">\n<div class=\"sources-list-content\">\n<div class=\"sources-list-title\">\n<p class=\"small-text-bold text-black sources-list-title-text\">Liste des sources<\/p>\n<div class=\"sources-expand-button-wrapper-mobile\">\n<div class=\"sources-expand-button\"><svg width=\"32\" height=\"32\" viewbox=\"0 0 32 32\" fill=\"none\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\"><path d=\"M8 12L16 20L24 12\" stroke=\"#8C9AAB\" stroke-width=\"2\" stroke-linecap=\"round\" stroke-linejoin=\"round\"><\/path><\/svg><\/div>\n<\/div>\n<\/div>\n<div class=\"sources-list-items\">\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">1.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\">Catalogue VOKA.<\/p>\n<p><span class=\"small-text-medium text-grey\">https:\/\/catalog.voka.io\/<\/span><\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">2.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\">The aberrant subclavian artery: approach to management. Karangelis D, Loggos S, Tzifa A, Mitropoulos FA. Curr Opin Cardiol. 2020 Nov;35(6):636-642. doi: 10.1097\/HCO.0000000000000793.    <\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">3.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\">Aberrant Subclavian Artery in Heritable Aortopathies: One Size Does Not Fit All. Isselbacher EM, Bloom JP. J Am Coll Cardiol. 2023 Mar 14;81(10):992-993. doi: 10.1016\/j.jacc.2023.01.020.    <\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">4.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\">Hybrid management of aberrant subclavian artery: A systematic review and meta-analysis. Kordzadeh A, Mouhsen MI, Chan DM, Singh A, Gadhvi VM. Vascular. 2024 Nov 28:17085381241303330. doi: 10.1177\/17085381241303330.    <\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">5.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\">A systematic review of open, hybrid, and endovascular repair of aberrant subclavian artery and Kommerell\u2019s diverticulum treatment. Loschi D, Santoro A, Rinaldi E, Bilman V, Chiesa R, Melissano G. J Vasc Surg. 2023 Feb;77(2):642-649.e4. doi: 10.1016\/j.jvs.2022.07.010.   <\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">6.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\">Surgical treatment of aberrant subclavian artery. Aslanov AD, Kalibatov RM, Logvina OE, Kardanova LY, Al-Ibrahim F. Khirurgiia (Mosk). 2023;(8):87-91. doi: 10.17116\/hirurgia202308187.   <\/p>\n<\/div>\n<\/div>\n<div class=\"source-item\">\n<p class=\"main-text-semibold text-black\">7.<\/p>\n<div class=\"source-item-content\">\n<p class=\"main-text-semibold text-black\">Characterization and surgical management of aberrant subclavian arteries. Tallarita T, Rogers RT, Bower TC, Stone W, Farres H, Money SR, Colglazier JJ. J Vasc Surg. 2023 Apr;77(4):1006-1015. doi: 10.1016\/j.jvs.2022.12.018.    <\/p>\n<\/div>\n<\/div>\n<\/div>\n<\/div>\n<div class=\"sources-expand-button-wrapper\">\n<div class=\"sources-expand-button\"><svg width=\"32\" height=\"32\" viewbox=\"0 0 32 32\" fill=\"none\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\"><path d=\"M8 12L16 20L24 12\" stroke=\"#8C9AAB\" stroke-width=\"2\" stroke-linecap=\"round\" stroke-linejoin=\"round\"><\/path><\/svg><\/div>\n<\/div>\n<\/div>\n","protected":false},"excerpt":{"rendered":"<p>L\u2019art\u00e8re subclavi\u00e8re droite aberrante (ASDA) est l\u2019anomalie la plus fr\u00e9quente de la crosse aortique, touchant environ 0,5 \u00e0 2 % de la population. Dans la grande majorit\u00e9 des cas, il s\u2019agit de l\u2019art\u00e8re subclavi\u00e8re droite aberrante (arteria lusoria). L\u2019anomalie peut \u00eatre d\u00e9tect\u00e9e \u00e0 tout \u00e2ge, mais le plus souvent, elle est diagnostiqu\u00e9e soit dans l\u2019enfance [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":0,"template":"","diseases_category":[234],"class_list":["post-622","diseases_post","type-diseases_post","status-publish","hentry","diseases_category-systeme-vasculaire"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v25.0 (Yoast SEO v26.5) - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Art\u00e8re subclavi\u00e8re aberrante : classification, diagnostic et traitement<\/title>\n<meta name=\"description\" content=\"L&#039;art\u00e8re subclavi\u00e8re droite aberrante est une anomalie fr\u00e9quente de la crosse aortique (plus souvent droite). 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